All ICD10 Codes
Chapter 17

Q00–Q99: Congenital Malformations, Deformations and Chromosomal Abnormalities

Congenital Malformations, Deformations and Chromosomal Abnormalities diagnostic classification updated for 2026.

Chapter Instructions

Excludes2(Not included here. Code separately if applicable.)
  • inborn errors of metabolism (E70-E88)
All CodesBillable Only
Internal Codes
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  • Q21.23—

    Complete atrioventricular septal defect

  • Q21.3—

    Tetralogy of Fallot

  • Q21.4—

    Aortopulmonary septal defect

  • Q21.8—

    Other congenital malformations of cardiac septa

  • Q21.9—

    Congenital malformation of cardiac septum, unspecified

  • Q22—

    Congenital malformations of pulmonary and tricuspid valves

  • Q22.0—

    Pulmonary valve atresia

  • Q22.1—

    Congenital pulmonary valve stenosis

  • Q22.2—

    Congenital pulmonary valve insufficiency

  • Q22.3—

    Other congenital malformations of pulmonary valve

  • Q22.4—

    Congenital tricuspid stenosis

  • Q22.5—

    Ebstein's anomaly

  • Q22.6—

    Hypoplastic right heart syndrome

  • Q22.8—

    Other congenital malformations of tricuspid valve

  • Q22.9—

    Congenital malformation of tricuspid valve, unspecified

  • Q23—

    Congenital malformations of aortic and mitral valves

  • Q23.0—

    Congenital stenosis of aortic valve

  • Q23.1—

    Congenital insufficiency of aortic valve

  • Q23.2—

    Congenital mitral stenosis

  • Q23.3—

    Congenital mitral insufficiency

  • Q23.4—

    Hypoplastic left heart syndrome

  • Q23.8—

    Other congenital malformations of aortic and mitral valves

  • Q23.81—

    Bicuspid aortic valve

  • Q23.82—

    Congenital mitral valve cleft leaflet

  • Q23.88—

    Other congenital malformations of aortic and mitral valves

  • Q23.9—

    Congenital malformation of aortic and mitral valves, unspecified

  • Q24—

    Other congenital malformations of heart

  • Q24.0—

    Dextrocardia

  • Q24.1—

    Levocardia

  • Q24.2—

    Cor triatriatum

  • Q24.3—

    Pulmonary infundibular stenosis

  • Q24.4—

    Congenital subaortic stenosis

  • Q24.5—

    Malformation of coronary vessels

  • Q24.6—

    Congenital heart block

  • Q24.8—

    Other specified congenital malformations of heart

  • Q24.9—

    Congenital malformation of heart, unspecified

  • Q25—

    Congenital malformations of great arteries

  • Q25.0—

    Patent ductus arteriosus

  • Q25.1—

    Coarctation of aorta

  • Q25.2—

    Atresia of aorta

  • Q25.21—

    Interruption of aortic arch

  • Q25.29—

    Other atresia of aorta

  • Q25.3—

    Supravalvular aortic stenosis

  • Q25.4—

    Other congenital malformations of aorta

  • Q25.40—

    Congenital malformation of aorta unspecified

  • Q25.41—

    Absence and aplasia of aorta

  • Q25.42—

    Hypoplasia of aorta

  • Q25.43—

    Congenital aneurysm of aorta

  • Q25.44—

    Congenital dilation of aorta

  • Q25.45—

    Double aortic arch

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