Q00–Q99: Congenital Malformations, Deformations and Chromosomal Abnormalities
Chapter 17 of ICD-10-CM 2027, 1,095 codes in 12 blocks.
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Chapter instructions
Excludes2: not included here, code separately if applicable
- inborn errors of metabolism (E70-E88)
Codes in this chapter
All codesBillable only1,095 results
- Q16.2Absence of eustachian tube
- Q16.3Congenital malformation of ear ossicles
- Q16.4Other congenital malformations of middle ear
- Q16.5Congenital malformation of inner ear
- Q16.9Congenital malformation of ear causing impairment of hearing, unspecified
- Q17Other congenital malformations of ear
- Q17.0Accessory auricle
- Q17.1Macrotia
- Q17.2Microtia
- Q17.3Other misshapen ear
- Q17.4Misplaced ear
- Q17.5Prominent ear
- Q17.8Other specified congenital malformations of ear
- Q17.9Congenital malformation of ear, unspecified
- Q18Other congenital malformations of face and neck
- Q18.0Sinus, fistula and cyst of branchial cleft
- Q18.1Preauricular sinus and cyst
- Q18.2Other branchial cleft malformations
- Q18.3Webbing of neck
- Q18.4Macrostomia
- Q18.5Microstomia
- Q18.6Macrocheilia
- Q18.7Microcheilia
- Q18.8Other specified congenital malformations of face and neck
- Q18.9Congenital malformation of face and neck, unspecified
- Q20Congenital malformations of cardiac chambers and connections
- Q20.0Common arterial trunk
- Q20.1Double outlet right ventricle
- Q20.2Double outlet left ventricle
- Q20.3Discordant ventriculoarterial connection
- Q20.4Double inlet ventricle
- Q20.5Discordant atrioventricular connection
- Q20.6Isomerism of atrial appendages
- Q20.8Other congenital malformations of cardiac chambers and connections
- Q20.9Congenital malformation of cardiac chambers and connections, unspecified
- Q21Congenital malformations of cardiac septa
- Q21.0Ventricular septal defect
- Q21.1Atrial septal defect
- Q21.10Atrial septal defect, unspecified
- Q21.11Secundum atrial septal defect
- Q21.12Patent foramen ovale
- Q21.13Coronary sinus atrial septal defect
- Q21.14Superior sinus venosus atrial septal defect
- Q21.15Inferior sinus venosus atrial septal defect
- Q21.16Sinus venosus atrial septal defect, unspecified
- Q21.19Other specified atrial septal defect
- Q21.2Atrioventricular septal defect
- Q21.20Atrioventricular septal defect, unspecified as to partial or complete
- Q21.21Partial atrioventricular septal defect
- Q21.22Transitional atrioventricular septal defect
