All ICD10 Codes
Chapter 17

Q00–Q99: Congenital Malformations, Deformations and Chromosomal Abnormalities

Congenital Malformations, Deformations and Chromosomal Abnormalities diagnostic classification updated for 2026.

Chapter Instructions

Excludes2(Not included here. Code separately if applicable.)
  • inborn errors of metabolism (E70-E88)
All CodesBillable Only
Internal Codes
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  • Q25.46—

    Tortuous aortic arch

  • Q25.47—

    Right aortic arch

  • Q25.48—

    Anomalous origin of subclavian artery

  • Q25.49—

    Other congenital malformations of aorta

  • Q25.5—

    Atresia of pulmonary artery

  • Q25.6—

    Stenosis of pulmonary artery

  • Q25.7—

    Other congenital malformations of pulmonary artery

  • Q25.71—

    Coarctation of pulmonary artery

  • Q25.72—

    Congenital pulmonary arteriovenous malformation

  • Q25.79—

    Other congenital malformations of pulmonary artery

  • Q25.8—

    Other congenital malformations of other great arteries

  • Q25.9—

    Congenital malformation of great arteries, unspecified

  • Q26—

    Congenital malformations of great veins

  • Q26.0—

    Congenital stenosis of vena cava

  • Q26.1—

    Persistent left superior vena cava

  • Q26.2—

    Total anomalous pulmonary venous connection

  • Q26.3—

    Partial anomalous pulmonary venous connection

  • Q26.4—

    Anomalous pulmonary venous connection, unspecified

  • Q26.5—

    Anomalous portal venous connection

  • Q26.6—

    Portal vein-hepatic artery fistula

  • Q26.8—

    Other congenital malformations of great veins

  • Q26.9—

    Congenital malformation of great vein, unspecified

  • Q27—

    Other congenital malformations of peripheral vascular system

  • Q27.0—

    Congenital absence and hypoplasia of umbilical artery

  • Q27.1—

    Congenital renal artery stenosis

  • Q27.2—

    Other congenital malformations of renal artery

  • Q27.3—

    Arteriovenous malformation (peripheral)

  • Q27.30—

    Arteriovenous malformation, site unspecified

  • Q27.31—

    Arteriovenous malformation of vessel of upper limb

  • Q27.32—

    Arteriovenous malformation of vessel of lower limb

  • Q27.33—

    Arteriovenous malformation of digestive system vessel

  • Q27.34—

    Arteriovenous malformation of renal vessel

  • Q27.39—

    Arteriovenous malformation, other site

  • Q27.4—

    Congenital phlebectasia

  • Q27.8—

    Other specified congenital malformations of peripheral vascular system

  • Q27.9—

    Congenital malformation of peripheral vascular system, unspecified

  • Q28—

    Other congenital malformations of circulatory system

  • Q28.0—

    Arteriovenous malformation of precerebral vessels

  • Q28.1—

    Other malformations of precerebral vessels

  • Q28.2—

    Arteriovenous malformation of cerebral vessels

  • Q28.3—

    Other malformations of cerebral vessels

  • Q28.8—

    Other specified congenital malformations of circulatory system

  • Q28.9—

    Congenital malformation of circulatory system, unspecified

  • Q30—

    Congenital malformations of nose

  • Q30.0—

    Choanal atresia

  • Q30.1—

    Agenesis and underdevelopment of nose

  • Q30.2—

    Fissured, notched and cleft nose

  • Q30.3—

    Congenital perforated nasal septum

  • Q30.8—

    Other congenital malformations of nose

  • Q30.9—

    Congenital malformation of nose, unspecified

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