All ICD10 Codes

Q00

Non-Billable
ChapterQ00–Q99
Rankcategory
Official Description

Anencephaly and similar malformations

Use a more specific code (3 billable)
Q00.0AnencephalyQ00.1CraniorachischisisQ00.2Iniencephaly
Metadata & Insights
  • •Non-billable category (requires more specific sub-code).
  • •Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (Q00-Q99).

CH17 Parent Instructions

Excludes2(Not included here. Code separately if applicable.)
  • inborn errors of metabolism (E70-E88)

Clinical Hierarchy

BillableHas subcodes
CH17Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0)
Q00-Q07Congenital malformations of the nervous system (Q00-Q07)
Q00Anencephaly and similar malformationsNot billable
Q00.0AnencephalyBillable
Q00.1CraniorachischisisBillable
Q00.2IniencephalyBillable

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to Q00:

chapterCH17
Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0)
View context instructions

MS-DRG Classification

2026

No direct MS-DRG triggers identified.

Cross Reference

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