N07Not billable, use a more specific code below

Hereditary nephropathy, not elsewhere classified

In Glomerular diseases (N00-N08), chapter 14: Diseases of the Genitourinary System

12 billable codes under N07: 5 are a CC; none map to an HCC.A CC or MCC (major CC) is a secondary diagnosis that raises the MS-DRG payment.

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Instructional notes

Excludes2: not included here, code separately if applicable

  • Alport's syndrome (Q87.81-)
  • hereditary amyloid nephropathy (E85.-)
  • nail patella syndrome (Q87.2)
  • non-neuropathic heredofamilial amyloidosis (E85.-)

Also applies, from Glomerular diseases (N00-N08)

These notes sit on N00-N08 and apply to every code under it, including N07.

Excludes1: not coded here, use a different code

  • hypertensive chronic kidney disease (I12.-)

Code also: add a code for this too, order depends on the encounter

  • any associated kidney failure (N17-N19).

Official coding guidelines

From the ICD-10-CM Official Guidelines for Coding and Reporting, FY 2027 (CMS and NCHS). Links open the PDF at the right page.

Covers chronic kidney disease staging, CKD in kidney transplant patients, and sequencing CKD with related conditions such as diabetes and hypertension.

Read Section I.C.14 (page 62)

N07 MS-DRGs

As the principal diagnosis, all 12 billable codes under N07 group to MS-DRG 698, 699, or 700 (v44.0). Which one applies depends on procedures performed, secondary diagnoses (CC/MCC), and the patient's age and discharge status.

About the condition

Plain-language background from MedlinePlus (National Library of Medicine), not coding guidance.

Genetic Disorders

Genetic disorders are health conditions caused by changes (also called mutations or variants) in your genes. Genes are parts of DNA found in your cells that carry instructions for how your body grows, develops, and functions. Many genes tell your body how to make proteins, which are needed for your body to work properly.

Read more about genetic disorders on MedlinePlus

Kidney Diseases

You have two kidneys, each about the size of your fist. They are near the middle of your back, just below the rib cage. Inside each kidney there are about a million tiny structures called nephrons. They filter your blood. They remove wastes and extra water, which become urine. The urine flows through tubes called ureters. It goes to your bladder, which stores the urine until you go to the bathroom.

Read more about kidney diseases on MedlinePlus

Code history

Valid since FY2016, when ICD-10-CM took effect on October 1, 2015. No changes since.