Chapter 10

J00–J99: Diseases of the Respiratory System

Diseases of the Respiratory System diagnostic classification updated for 2026.

Chapter Instructions

Excludes2(Not included here. Code separately if applicable.)
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • smoke inhalation (T59.81-)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Use Additional Code
  • code, where applicable, to identify:
  • exposure to environmental tobacco smoke (Z77.22)
  • exposure to tobacco smoke in the perinatal period (P96.81)
  • history of tobacco dependence (Z87.891)
  • occupational exposure to environmental tobacco smoke (Z57.31)
  • tobacco dependence (F17.-)
  • tobacco use (Z72.0)
Internal Codes
  • J67.8

    Hypersensitivity pneumonitis due to other organic dusts

  • J67.9

    Hypersensitivity pneumonitis due to unspecified organic dust

  • J68

    Respiratory conditions due to inhalation of chemicals, gases, fumes and vapors

  • J68.0

    Bronchitis and pneumonitis due to chemicals, gases, fumes and vapors

  • J68.1

    Pulmonary edema due to chemicals, gases, fumes and vapors

  • J68.2

    Upper respiratory inflammation due to chemicals, gases, fumes and vapors, not elsewhere classified

  • J68.3

    Other acute and subacute respiratory conditions due to chemicals, gases, fumes and vapors

  • J68.4

    Chronic respiratory conditions due to chemicals, gases, fumes and vapors

  • J68.8

    Other respiratory conditions due to chemicals, gases, fumes and vapors

  • J68.9

    Unspecified respiratory condition due to chemicals, gases, fumes and vapors

  • J69

    Pneumonitis due to solids and liquids

  • J69.0

    Pneumonitis due to inhalation of food and vomit

  • J69.1

    Pneumonitis due to inhalation of oils and essences

  • J69.8

    Pneumonitis due to inhalation of other solids and liquids

  • J70

    Respiratory conditions due to other external agents

  • J70.0

    Acute pulmonary manifestations due to radiation

  • J70.1

    Chronic and other pulmonary manifestations due to radiation

  • J70.2

    Acute drug-induced interstitial lung disorders

  • J70.3

    Chronic drug-induced interstitial lung disorders

  • J70.4

    Drug-induced interstitial lung disorders, unspecified

  • J70.5

    Respiratory conditions due to smoke inhalation

  • J70.8

    Respiratory conditions due to other specified external agents

  • J70.9

    Respiratory conditions due to unspecified external agent

  • J80

    Acute respiratory distress syndrome

  • J81

    Pulmonary edema

  • J81.0

    Acute pulmonary edema

  • J81.1

    Chronic pulmonary edema

  • J82

    Pulmonary eosinophilia, not elsewhere classified

  • J82.8

    Pulmonary eosinophilia, not elsewhere classified

  • J82.81

    Chronic eosinophilic pneumonia

  • J82.82

    Acute eosinophilic pneumonia

  • J82.83

    Eosinophilic asthma

  • J82.89

    Other pulmonary eosinophilia, not elsewhere classified

  • J84

    Other interstitial pulmonary diseases

  • J84.0

    Alveolar and parieto-alveolar conditions

  • J84.01

    Alveolar proteinosis

  • J84.02

    Pulmonary alveolar microlithiasis

  • J84.03

    Idiopathic pulmonary hemosiderosis

  • J84.09

    Other alveolar and parieto-alveolar conditions

  • J84.1

    Other interstitial pulmonary diseases with fibrosis

  • J84.10

    Pulmonary fibrosis, unspecified

  • J84.11

    Idiopathic interstitial pneumonia

  • J84.111

    Idiopathic interstitial pneumonia, not otherwise specified

  • J84.112

    Idiopathic pulmonary fibrosis

  • J84.113

    Idiopathic non-specific interstitial pneumonitis

  • J84.114

    Acute interstitial pneumonitis

  • J84.115

    Respiratory bronchiolitis interstitial lung disease

  • J84.116

    Cryptogenic organizing pneumonia

  • J84.117

    Desquamative interstitial pneumonia

  • J84.17

    Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere

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