Chapter 9

I00–I99: Diseases of the Circulatory System

Diseases of the Circulatory System diagnostic classification updated for 2026.

Chapter Instructions

Excludes2(Not included here. Code separately if applicable.)
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
  • systemic connective tissue disorders (M30-M36)
  • transient cerebral ischemic attacks and related syndromes (G45.-)
Internal Codes
  • I16.1

    Hypertensive emergency

  • I16.9

    Hypertensive crisis, unspecified

  • I1A.0

    Resistant hypertension

  • I20.0

    Unstable angina

  • I20.1

    Angina pectoris with documented spasm

  • I20.2

    Refractory angina pectoris

  • I20.81

    Angina pectoris with coronary microvascular dysfunction

  • I20.89

    Other forms of angina pectoris

  • I20.9

    Angina pectoris, unspecified

  • I21.01

    ST elevation (STEMI) myocardial infarction involving left main coronary artery

  • I21.02

    ST elevation (STEMI) myocardial infarction involving left anterior descending coronary artery

  • I21.09

    ST elevation (STEMI) myocardial infarction involving other coronary artery of anterior wall

  • I21.11

    ST elevation (STEMI) myocardial infarction involving right coronary artery

  • I21.19

    ST elevation (STEMI) myocardial infarction involving other coronary artery of inferior wall

  • I21.21

    ST elevation (STEMI) myocardial infarction involving left circumflex coronary artery

  • I21.29

    ST elevation (STEMI) myocardial infarction involving other sites

  • I21.3

    ST elevation (STEMI) myocardial infarction of unspecified site

  • I21.4

    Non-ST elevation (NSTEMI) myocardial infarction

  • I21.9

    Acute myocardial infarction, unspecified

  • I21.A1

    Myocardial infarction type 2

  • I21.A9

    Other myocardial infarction type

  • I21.B

    Myocardial infarction with coronary microvascular dysfunction

  • I22.0

    Subsequent ST elevation (STEMI) myocardial infarction of anterior wall

  • I22.1

    Subsequent ST elevation (STEMI) myocardial infarction of inferior wall

  • I22.2

    Subsequent non-ST elevation (NSTEMI) myocardial infarction

  • I22.8

    Subsequent ST elevation (STEMI) myocardial infarction of other sites

  • I22.9

    Subsequent ST elevation (STEMI) myocardial infarction of unspecified site

  • I23.0

    Hemopericardium as current complication following acute myocardial infarction

  • I23.1

    Atrial septal defect as current complication following acute myocardial infarction

  • I23.2

    Ventricular septal defect as current complication following acute myocardial infarction

  • I23.3

    Rupture of cardiac wall without hemopericardium as current complication following acute myocardial infarction

  • I23.4

    Rupture of chordae tendineae as current complication following acute myocardial infarction

  • I23.5

    Rupture of papillary muscle as current complication following acute myocardial infarction

  • I23.6

    Thrombosis of atrium, auricular appendage, and ventricle as current complications following acute myocardial infarction

  • I23.7

    Postinfarction angina

  • I23.8

    Other current complications following acute myocardial infarction

  • I24.0

    Acute coronary thrombosis not resulting in myocardial infarction

  • I24.1

    Dressler's syndrome

  • I24.81

    Acute coronary microvascular dysfunction

  • I24.89

    Other forms of acute ischemic heart disease

  • I24.9

    Acute ischemic heart disease, unspecified

  • I25.10

    Atherosclerotic heart disease of native coronary artery without angina pectoris

  • I25.110

    Atherosclerotic heart disease of native coronary artery with unstable angina pectoris

  • I25.111

    Atherosclerotic heart disease of native coronary artery with angina pectoris with documented spasm

  • I25.112

    Atherosclerotic heart disease of native coronary artery with refractory angina pectoris

  • I25.118

    Atherosclerotic heart disease of native coronary artery with other forms of angina pectoris

  • I25.119

    Atherosclerotic heart disease of native coronary artery with unspecified angina pectoris

  • I25.2

    Old myocardial infarction

  • I25.3

    Aneurysm of heart

  • I25.41

    Coronary artery aneurysm

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