Chapter 6

G00–G99: Diseases of the Nervous System

Diseases of the Nervous System diagnostic classification updated for 2026.

Chapter Instructions

Excludes2(Not included here. Code separately if applicable.)
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Internal Codes
  • G37.9|

    Demyelinating disease of central nervous system, unspecified

  • G40.001|

    Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset, not intractable, with status epilepticus

  • G40.009|

    Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset, not intractable, without status epilepticus

  • G40.011|

    Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset, intractable, with status epilepticus

  • G40.019|

    Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset, intractable, without status epilepticus

  • G40.101|

    Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, not intractable, with status epilepticus

  • G40.109|

    Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, not intractable, without status epilepticus

  • G40.111|

    Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, intractable, with status epilepticus

  • G40.119|

    Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, intractable, without status epilepticus

  • G40.201|

    Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, not intractable, with status epilepticus

  • G40.209|

    Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, not intractable, without status epilepticus

  • G40.211|

    Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, intractable, with status epilepticus

  • G40.219|

    Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, intractable, without status epilepticus

  • G40.301|

    Generalized idiopathic epilepsy and epileptic syndromes, not intractable, with status epilepticus

  • G40.309|

    Generalized idiopathic epilepsy and epileptic syndromes, not intractable, without status epilepticus

  • G40.311|

    Generalized idiopathic epilepsy and epileptic syndromes, intractable, with status epilepticus

  • G40.319|

    Generalized idiopathic epilepsy and epileptic syndromes, intractable, without status epilepticus

  • G40.401|

    Other generalized epilepsy and epileptic syndromes, not intractable, with status epilepticus

  • G40.409|

    Other generalized epilepsy and epileptic syndromes, not intractable, without status epilepticus

  • G40.411|

    Other generalized epilepsy and epileptic syndromes, intractable, with status epilepticus

  • G40.419|

    Other generalized epilepsy and epileptic syndromes, intractable, without status epilepticus

  • G40.42|

    Cyclin-Dependent Kinase-Like 5 Deficiency Disorder

  • G40.501|

    Epileptic seizures related to external causes, not intractable, with status epilepticus

  • G40.509|

    Epileptic seizures related to external causes, not intractable, without status epilepticus

  • G40.801|

    Other epilepsy, not intractable, with status epilepticus

  • G40.802|

    Other epilepsy, not intractable, without status epilepticus

  • G40.803|

    Other epilepsy, intractable, with status epilepticus

  • G40.804|

    Other epilepsy, intractable, without status epilepticus

  • G40.811|

    Lennox-Gastaut syndrome, not intractable, with status epilepticus

  • G40.812|

    Lennox-Gastaut syndrome, not intractable, without status epilepticus

  • G40.813|

    Lennox-Gastaut syndrome, intractable, with status epilepticus

  • G40.814|

    Lennox-Gastaut syndrome, intractable, without status epilepticus

  • G40.821|

    Epileptic spasms, not intractable, with status epilepticus

  • G40.822|

    Epileptic spasms, not intractable, without status epilepticus

  • G40.823|

    Epileptic spasms, intractable, with status epilepticus

  • G40.824|

    Epileptic spasms, intractable, without status epilepticus

  • G40.833|

    Dravet syndrome, intractable, with status epilepticus

  • G40.834|

    Dravet syndrome, intractable, without status epilepticus

  • G40.841|

    KCNQ2-related epilepsy, not intractable, with status epilepticus

  • G40.842|

    KCNQ2-related epilepsy, not intractable, without status epilepticus

  • G40.843|

    KCNQ2-related epilepsy, intractable, with status epilepticus

  • G40.844|

    KCNQ2-related epilepsy, intractable, without status epilepticus

  • G40.89|

    Other seizures

  • G40.901|

    Epilepsy, unspecified, not intractable, with status epilepticus

  • G40.909|

    Epilepsy, unspecified, not intractable, without status epilepticus

  • G40.911|

    Epilepsy, unspecified, intractable, with status epilepticus

  • G40.919|

    Epilepsy, unspecified, intractable, without status epilepticus

  • G40.A01|

    Absence epileptic syndrome, not intractable, with status epilepticus

  • G40.A09|

    Absence epileptic syndrome, not intractable, without status epilepticus

  • G40.A11|

    Absence epileptic syndrome, intractable, with status epilepticus

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