Chapter 6

G00–G99: Diseases of the Nervous System

Diseases of the Nervous System diagnostic classification updated for 2026.

Chapter Instructions

Excludes2(Not included here. Code separately if applicable.)
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Internal Codes
  • G71.0340

    Limb girdle muscular dystrophy due to sarcoglycan dysfunction, unspecified

  • G71.0341

    Limb girdle muscular dystrophy due to alpha sarcoglycan dysfunction

  • G71.0342

    Limb girdle muscular dystrophy due to beta sarcoglycan dysfunction

  • G71.0349

    Limb girdle muscular dystrophy due to other sarcoglycan dysfunction

  • G71.035

    Limb girdle muscular dystrophy due to anoctamin-5 dysfunction

  • G71.036

    Limb girdle muscular dystrophy due to fukutin related protein dysfunction

  • G71.038

    Other limb girdle muscular dystrophy

  • G71.039

    Limb girdle muscular dystrophy, unspecified

  • G71.09

    Other specified muscular dystrophies

  • G71.11

    Myotonic muscular dystrophy

  • G71.12

    Myotonia congenita

  • G71.13

    Myotonic chondrodystrophy

  • G71.14

    Drug induced myotonia

  • G71.19

    Other specified myotonic disorders

  • G71.20

    Congenital myopathy, unspecified

  • G71.21

    Nemaline myopathy

  • G71.220

    X-linked myotubular myopathy

  • G71.228

    Other centronuclear myopathy

  • G71.29

    Other congenital myopathy

  • G71.3

    Mitochondrial myopathy, not elsewhere classified

  • G71.8

    Other primary disorders of muscles

  • G71.9

    Primary disorder of muscle, unspecified

  • G72.0

    Drug-induced myopathy

  • G72.1

    Alcoholic myopathy

  • G72.2

    Myopathy due to other toxic agents

  • G72.3

    Periodic paralysis

  • G72.41

    Inclusion body myositis [IBM]

  • G72.49

    Other inflammatory and immune myopathies, not elsewhere classified

  • G72.81

    Critical illness myopathy

  • G72.89

    Other specified myopathies

  • G72.9

    Myopathy, unspecified

  • G73.1

    Lambert-Eaton syndrome in neoplastic disease

  • G73.3

    Myasthenic syndromes in other diseases classified elsewhere

  • G73.7

    Myopathy in diseases classified elsewhere

  • G80.0

    Spastic quadriplegic cerebral palsy

  • G80.1

    Spastic diplegic cerebral palsy

  • G80.2

    Spastic hemiplegic cerebral palsy

  • G80.3

    Athetoid cerebral palsy

  • G80.4

    Ataxic cerebral palsy

  • G80.8

    Other cerebral palsy

  • G80.9

    Cerebral palsy, unspecified

  • G81.00

    Flaccid hemiplegia affecting unspecified side

  • G81.01

    Flaccid hemiplegia affecting right dominant side

  • G81.02

    Flaccid hemiplegia affecting left dominant side

  • G81.03

    Flaccid hemiplegia affecting right nondominant side

  • G81.04

    Flaccid hemiplegia affecting left nondominant side

  • G81.10

    Spastic hemiplegia affecting unspecified side

  • G81.11

    Spastic hemiplegia affecting right dominant side

  • G81.12

    Spastic hemiplegia affecting left dominant side

  • G81.13

    Spastic hemiplegia affecting right nondominant side

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