G71.3

Billable
ChapterG00–G99
Ranksubcategory
Official Description

Mitochondrial myopathy, not elsewhere classified

Metadata & Insights
  • Billable/specific code (valid for reimbursement).
  • Chapter 6: Diseases of the Nervous System (G00-G99).

Instructional Notes

Excludes1(Not coded here. Use a different code.)
  • Kearns-Sayre syndrome (H49.81)
  • Leber's disease (H47.21)
  • Leigh's encephalopathy (G31.82)
  • mitochondrial metabolism disorders (E88.4.-)
  • Reye's syndrome (G93.7)
General instructions are available for the parent sections:

Clinical Hierarchy

BillableHas subcodes
CH6Diseases of the nervous system (G00-G99)
G70-G73Diseases of myoneural junction and muscle (G70-G73)
G71Primary disorders of muscles
G71.3Mitochondrial myopathy, not elsewhere classifiedBillable

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to G71.3:

categoryG71
Primary disorders of muscles
View context instructions
chapterCH6
Diseases of the nervous system (G00-G99)
View context instructions

MS-DRG Classification

2026 v43.1

Cross Reference

Find Procedures (ICD-10-PCS)

Find surgical and procedural codes related to Mitochondrial myopathy, not elsewhere classified.

Search PCS Codes