Chapter 4

E00–E89: Endocrine, Nutritional and Metabolic Diseases

Endocrine, Nutritional and Metabolic Diseases diagnostic classification updated for 2026.

Chapter Instructions

Excludes1(Not coded here. Use a different code.)
  • transitory endocrine and metabolic disorders specific to newborn (P70-P74)
Internal Codes
  • E83.41

    Hypermagnesemia

  • E83.42

    Hypomagnesemia

  • E83.49

    Other disorders of magnesium metabolism

  • E83.50

    Unspecified disorder of calcium metabolism

  • E83.51

    Hypocalcemia

  • E83.52

    Hypercalcemia

  • E83.59

    Other disorders of calcium metabolism

  • E83.81

    Hungry bone syndrome

  • E83.820

    Generalized arterial calcification of infancy with unspecified genetic causality

  • E83.821

    ENPP1 deficiency causing generalized arterial calcification of infancy

  • E83.822

    ENPP1 deficiency causing autosomal recessive hypophosphatemic rickets type 2

  • E83.823

    ABCC6 deficiency causing generalized arterial calcification of infancy

  • E83.824

    ABCC6 deficiency causing pseudoxanthoma elasticum

  • E83.825

    CD73 deficiency causing arterial calcification

  • E83.89

    Other disorders of mineral metabolism

  • E83.9

    Disorder of mineral metabolism, unspecified

  • E84.0

    Cystic fibrosis with pulmonary manifestations

  • E84.11

    Meconium ileus in cystic fibrosis

  • E84.19

    Cystic fibrosis with other intestinal manifestations

  • E84.8

    Cystic fibrosis with other manifestations

  • E84.9

    Cystic fibrosis, unspecified

  • E85.0

    Non-neuropathic heredofamilial amyloidosis

  • E85.1

    Neuropathic heredofamilial amyloidosis

  • E85.2

    Heredofamilial amyloidosis, unspecified

  • E85.3

    Secondary systemic amyloidosis

  • E85.4

    Organ-limited amyloidosis

  • E85.81

    Light chain (AL) amyloidosis

  • E85.82

    Wild-type transthyretin-related (ATTR) amyloidosis

  • E85.89

    Other amyloidosis

  • E85.9

    Amyloidosis, unspecified

  • E86.0

    Dehydration

  • E86.1

    Hypovolemia

  • E86.9

    Volume depletion, unspecified

  • E87.0

    Hyperosmolality and hypernatremia

  • E87.1

    Hypo-osmolality and hyponatremia

  • E87.20

    Acidosis, unspecified

  • E87.21

    Acute metabolic acidosis

  • E87.22

    Chronic metabolic acidosis

  • E87.29

    Other acidosis

  • E87.3

    Alkalosis

  • E87.4

    Mixed disorder of acid-base balance

  • E87.5

    Hyperkalemia

  • E87.6

    Hypokalemia

  • E87.70

    Fluid overload, unspecified

  • E87.71

    Transfusion associated circulatory overload

  • E87.79

    Other fluid overload

  • E87.8

    Other disorders of electrolyte and fluid balance, not elsewhere classified

  • E88.01

    Alpha-1-antitrypsin deficiency

  • E88.02

    Plasminogen deficiency

  • E88.09

    Other disorders of plasma-protein metabolism, not elsewhere classified

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