E71.542

Billable
ChapterE00–E89
Ranksubcategory
Official Description

Other group 3 peroxisomal disorders

Metadata & Insights
  • •2026 ICD-10-CM Edition - Effective October 1, 2025.
  • •Billable/specific code (valid for reimbursement).
  • •Chapter 4: Endocrine, Nutritional and Metabolic Diseases (E00-E89).
General instructions are available for the parent sections:
View CH4 NotesView E70-E88 NotesView E71.5 Notes

Clinical Hierarchy

CH4Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88Metabolic disorders (E70-E88)
E71Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
E71.5Peroxisomal disorders
E71.54Other peroxisomal disorders
E71.542Other group 3 peroxisomal disorders

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to E71.542:

subcategoryE71.5
Peroxisomal disorders
View context instructions
blockE70-E88
Metabolic disorders (E70-E88)
View context instructions
chapterCH4
Endocrine, nutritional and metabolic diseases (E00-E89)
View context instructions

Alphabetic Index Mentions

These are Diagnosis Index lookup paths that route to E71.542. Use them as entry terms for search, then confirm final coding instructions in the Tabular List and notes above.

1 raw paths
Disorder (of)1 unique routes
peroxisomal
specified form NEC
group 3→E71.542

MS-DRG Classification

2026 v43.1

This code is grouped within the following Diagnosis Related Group(s) for clinical reimbursement:

DRG 642
Inborn and Other Disorders of Metabolism

Cross Reference

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