E71.54

Non-Billable

ChapterE00–E89

Ranksubcategory

Official Description

Other peroxisomal disorders

Metadata & Insights

•2026 ICD-10-CM Edition - Effective October 1, 2025.
•Non-billable category (requires more specific sub-code).
•Chapter 4: Endocrine, Nutritional and Metabolic Diseases (E00-E89).

General instructions are available for the parent sections:

View CH4 Notes View E70-E88 Notes View E71.5 Notes

Clinical Hierarchy

CH4Endocrine, nutritional and metabolic diseases (E00-E89)

E70-E88Metabolic disorders (E70-E88)

E71Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism

E71.5Peroxisomal disorders

E71.54Other peroxisomal disorders

E71.540Rhizomelic chondrodysplasia punctata

E71.541Zellweger-like syndrome

E71.542Other group 3 peroxisomal disorders

E71.548Other peroxisomal disorders

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to E71.54:

subcategoryE71.5

Peroxisomal disorders

View context instructions

blockE70-E88

Metabolic disorders (E70-E88)

View context instructions

chapterCH4

Endocrine, nutritional and metabolic diseases (E00-E89)

View context instructions

Alphabetic Index Mentions

These are Diagnosis Index lookup paths that route to E71.54. Use them as entry terms for search, then confirm final coding instructions in the Tabular List and notes above.

6 raw paths

Disorder (of)4 unique routes

peroxisomal(4 variants)

rhizomelic chondrodysplasia punctata→E71.54

specified form NEC→E71.54(2 variants)

group 3→E71.54

Zellweger-like syndrome→E71.54

Rhizomelic chondrodysplasia punctata1 unique routes

Direct index entry→E71.54

Syndrome1 unique routes

Zellweger-like syndrome→E71.54

MS-DRG Classification

2026

No direct MS-DRG triggers identified.

Cross Reference

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