E00.1

Billable
ChapterE00–E89
Ranksubcategory
Official Description

Congenital iodine-deficiency syndrome, myxedematous type

Metadata & Insights
  • •2026 ICD-10-CM Edition - Effective October 1, 2025.
  • •Billable/specific code (valid for reimbursement).
  • •Chapter 4: Endocrine, Nutritional and Metabolic Diseases (E00-E89).

Instructional Notes

Includes
  • Endemic hypothyroid cretinism
  • Endemic cretinism, myxedematous type
General instructions are available for the parent sections:
View CH4 NotesView E00 Notes

Clinical Hierarchy

CH4Endocrine, nutritional and metabolic diseases (E00-E89)
E00-E07Disorders of thyroid gland (E00-E07)
E00Congenital iodine-deficiency syndrome
E00.1Congenital iodine-deficiency syndrome, myxedematous type

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to E00.1:

categoryE00
Congenital iodine-deficiency syndrome
View context instructions
chapterCH4
Endocrine, nutritional and metabolic diseases (E00-E89)
View context instructions

Alphabetic Index Mentions

These are Diagnosis Index lookup paths that route to E00.1. Use them as entry terms for search, then confirm final coding instructions in the Tabular List and notes above.

4 raw paths
Cretin, cretinism (congenital) (endemic) (nongoitrous) (sporadic)2 unique routes
type(2 variants)
hypothyroid→E00.1
myxedematous→E00.1
Myxedema (adult) (idiocy) (infantile) (juvenile)1 unique routes
congenital→E00.1
Syndrome1 unique routes
iodine-deficiency, congenital
type
myxedematous→E00.1

MS-DRG Classification

2026 v43.1

This code is grouped within the following Diagnosis Related Group(s) for clinical reimbursement:

DRG 643
Endocrine Disorders with MCC
DRG 644
Endocrine Disorders with CC
DRG 645
Endocrine Disorders without CC/MCC

Cross Reference

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