D82.1

Billable
ChapterD50–D89
Ranksubcategory
Official Description

Di George's syndrome

Metadata & Insights
  • •2026 ICD-10-CM Edition - Effective October 1, 2025.
  • •Billable/specific code (valid for reimbursement).
  • •Chapter 3: Diseases of the Blood and Blood-Forming Organs (D50-D89).

Instructional Notes

Includes
  • Pharyngeal pouch syndrome
  • Thymic alymphoplasia
  • Thymic aplasia or hypoplasia with immunodeficiency
General instructions are available for the parent sections:
View CH3 NotesView D80-D89 NotesView D82 Notes

Clinical Hierarchy

CH3Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
D80-D89Certain disorders involving the immune mechanism (D80-D89)
D82Immunodeficiency associated with other major defects
D82.1Di George's syndrome

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to D82.1:

categoryD82
Immunodeficiency associated with other major defects
View context instructions
blockD80-D89
Certain disorders involving the immune mechanism (D80-D89)
View context instructions
chapterCH3
Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
View context instructions

Alphabetic Index Mentions

These are Diagnosis Index lookup paths that route to D82.1. Use them as entry terms for search, then confirm final coding instructions in the Tabular List and notes above.

12 raw paths
Alymphocytosis1 unique routes
thymic (with immunodeficiency)→D82.1
Alymphoplasia, thymic1 unique routes
Direct index entry→D82.1
Aplasia2 unique routes
parathyroid-thymic→D82.1
thymic, with immunodeficiency→D82.1
Di George's syndrome1 unique routes
Direct index entry→D82.1
DiGeorge's syndrome (thymic hypoplasia)1 unique routes
Direct index entry→D82.1
Dysplasia1 unique routes
thymic, with immunodeficiency→D82.1
Hypoplasia, hypoplastic2 unique routes
thymic, with immunodeficiency→D82.1
thymus (gland)
with immunodeficiency→D82.1
Pharyngeal pouch syndrome1 unique routes
Direct index entry→D82.1
Syndrome2 unique routes
di George's→D82.1
pharyngeal pouch→D82.1

MS-DRG Classification

2026 v43.1

This code is grouped within the following Diagnosis Related Group(s) for clinical reimbursement:

DRG 808
Major Hematological and Immunological Diagnoses Except Sickle Cell Crisis and Coagulation Disorders with MCC
DRG 809
Major Hematological and Immunological Diagnoses Except Sickle Cell Crisis and Coagulation Disorders with CC
DRG 810
Major Hematological and Immunological Diagnoses Except Sickle Cell Crisis and Coagulation Disorders without CC/MCC

Cross Reference

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