Q07.0

Non-Billable

ChapterQ00–Q99

Ranksubcategory

Official Description

Arnold-Chiari syndrome

Metadata & Insights

•2026 ICD-10-CM Edition - Effective October 1, 2025.
•Non-billable category (requires more specific sub-code).
•Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (Q00-Q99).

Instructional Notes

Includes

Arnold-Chiari syndrome, type II

Excludes1(Not coded here)

Arnold-Chiari syndrome, type III (Q01.-)
Arnold-Chiari syndrome, type IV (Q04.8)

General instructions are available for the parent sections:

View CH17 Notes View Q07 Notes

Clinical Hierarchy

CH17Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0)

Q00-Q07Congenital malformations of the nervous system (Q00-Q07)

Q07Other congenital malformations of nervous system

Q07.0Arnold-Chiari syndrome

Q07.00Arnold-Chiari syndrome without spina bifida or hydrocephalus

Q07.01Arnold-Chiari syndrome with spina bifida

Q07.02Arnold-Chiari syndrome with hydrocephalus

Q07.03Arnold-Chiari syndrome with spina bifida and hydrocephalus

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to Q07.0:

categoryQ07

Other congenital malformations of nervous system

View context instructions

chapterCH17

Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0)

View context instructions

Alphabetic Index Mentions

These are Diagnosis Index lookup paths that route to Q07.0. Use them as entry terms for search, then confirm final coding instructions in the Tabular List and notes above.

7 raw paths

Arnold-Chiari disease, obstruction or syndrome (type II)5 unique routes

Direct index entry→Q07.0

with(4 variants)

hydrocephalus→Q07.0(2 variants)

with spina bifida→Q07.0

spina bifida→Q07.0(2 variants)

with hydrocephalus→Q07.0

Malformation (congenital)1 unique routes

Chiari

Type II→Q07.0

Syndrome1 unique routes