Q04.8

Billable
ChapterQ00–Q99
Ranksubcategory
Official Description

Other specified congenital malformations of brain

Metadata & Insights
  • •2026 ICD-10-CM Edition - Effective October 1, 2025.
  • •Billable/specific code (valid for reimbursement).
  • •Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (Q00-Q99).

Instructional Notes

Includes
  • Arnold-Chiari syndrome, type IV
  • Macrogyria
General instructions are available for the parent sections:
View CH17 NotesView Q04 Notes

Clinical Hierarchy

CH17Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0)
Q00-Q07Congenital malformations of the nervous system (Q00-Q07)
Q04Other congenital malformations of brain
Q04.8Other specified congenital malformations of brain

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to Q04.8:

categoryQ04
Other congenital malformations of brain
View context instructions
chapterCH17
Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0)
View context instructions

Alphabetic Index Mentions

These are Diagnosis Index lookup paths that route to Q04.8. Use them as entry terms for search, then confirm final coding instructions in the Tabular List and notes above.

16 raw paths
Anomaly, anomalous (congenital) (unspecified type)1 unique routes
meninges
cerebral→Q04.8
Arnold-Chiari disease, obstruction or syndrome (type II)1 unique routes
type IV→Q04.8
Deformity1 unique routes
meninges or membrane (congenital)
cerebral→Q04.8
Dilatation1 unique routes
ventricular, ventricle (acute) (chronic)
cerebral, congenital→Q04.8
Displacement, displaced2 unique routes
brain stem, caudal (congenital)→Q04.8
cerebellum, caudal (congenital)→Q04.8
Distortion (s) (congenital)1 unique routes
gyri→Q04.8
Ectopic, ectopia (congenital)2 unique routes
brain→Q04.8
cerebral→Q04.8
Heterotopia, heterotopic1 unique routes
cerebralis→Q04.8
Macrogyria (congenital)1 unique routes
Direct index entry→Q04.8
Malformation (congenital)2 unique routes
brain (multiple)
specified type NEC→Q04.8
meninges or membrane (congenital)
cerebral→Q04.8
Malposition1 unique routes
congenital
brain tissue→Q04.8
Softening1 unique routes
brain (necrotic) (progressive)
congenital→Q04.8
Ulegyria1 unique routes
Direct index entry→Q04.8

MS-DRG Classification

2026 v43.1

This code is grouped within the following Diagnosis Related Group(s) for clinical reimbursement:

DRG 091
Other Disorders of Nervous System with MCC
DRG 092
Other Disorders of Nervous System with CC
DRG 093
Other Disorders of Nervous System without CC/MCC
DRG 791
Prematurity with Major Problems
DRG 793
Full Term Neonate with Major Problems

Cross Reference

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