Q01

Non-Billable

ChapterQ00–Q99

Rankcategory

Official Description

Encephalocele

Metadata & Insights

•2026 ICD-10-CM Edition - Effective October 1, 2025.
•Non-billable category (requires more specific sub-code).
•Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (Q00-Q99).

CH17 Parent Instructions

Excludes2(Not included here)

inborn errors of metabolism (E70-E88)

Instructional Notes

Includes

Arnold-Chiari syndrome, type III
encephalocystocele
encephalomyelocele
hydroencephalocele
hydromeningocele, cranial
meningocele, cerebral
meningoencephalocele

Excludes1(Not coded here)

Meckel-Gruber syndrome (Q61.9)

Clinical Hierarchy

CH17Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0)

Q00-Q07Congenital malformations of the nervous system (Q00-Q07)

Q01Encephalocele

Q01.0Frontal encephalocele

Q01.1Nasofrontal encephalocele

Q01.2Occipital encephalocele

Q01.8Encephalocele of other sites

Q01.9Encephalocele, unspecified

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to Q01:

chapterCH17

Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0)

View context instructions

Alphabetic Index Mentions

These are Diagnosis Index lookup paths that route to Q01. Use them as entry terms for search, then confirm final coding instructions in the Tabular List and notes above.

9 raw paths

Encephalocele5 unique routes

Direct index entry→Q01

frontal→Q01

nasofrontal→Q01

occipital→Q01

specified NEC→Q01

Hernia, hernial (acquired) (recurrent)2 unique routes

cerebral, congenital

endaural→Q01

foramen magnum

congenital→Q01