Q03

Non-Billable
ChapterQ00–Q99
Rankcategory
Official Description

Congenital hydrocephalus

Metadata & Insights
  • •2026 ICD-10-CM Edition - Effective October 1, 2025.
  • •Non-billable category (requires more specific sub-code).
  • •Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (Q00-Q99).

CH17 Parent Instructions

Excludes2(Not included here)
  • inborn errors of metabolism (E70-E88)

Instructional Notes

Includes
  • hydrocephalus in newborn
Excludes1(Not coded here)
  • Arnold-Chiari syndrome, type II (Q07.0-)
  • acquired hydrocephalus (G91.-)
  • hydrocephalus due to congenital toxoplasmosis (P37.1)
  • hydrocephalus with spina bifida (Q05.0-Q05.4)

Clinical Hierarchy

CH17Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0)
Q00-Q07Congenital malformations of the nervous system (Q00-Q07)
Q03Congenital hydrocephalus
Q03.0Malformations of aqueduct of Sylvius
Q03.1Atresia of foramina of Magendie and Luschka
Q03.8Other congenital hydrocephalus
Q03.9Congenital hydrocephalus, unspecified

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to Q03:

chapterCH17
Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0)
View context instructions

Alphabetic Index Mentions

These are Diagnosis Index lookup paths that route to Q03. Use them as entry terms for search, then confirm final coding instructions in the Tabular List and notes above.

25 raw paths
Absence (of) (organ or part) (complete or partial)1 unique routes
skull bone (congenital)
with
hydrocephalus→Q03
Agenesis1 unique routes
skull (bone)
with
hydrocephalus→Q03
Anomaly, anomalous (congenital) (unspecified type)3 unique routes
aqueduct of Sylvius→Q03
bone
skull
with
hydrocephalus→Q03
skull
with
hydrocephalus→Q03
Atresia, atretic3 unique routes
aqueduct of Sylvius→Q03
foramen of(2 variants)
Luschka→Q03
Magendie→Q03
Block, blocked1 unique routes
foramen Magendie (acquired)
congenital→Q03
Cyst (colloid) (mucous) (simple) (retention)1 unique routes
Dandy-Walker→Q03
Dandy-Walker syndrome1 unique routes
Direct index entry→Q03
Deformity2 unique routes
Dandy-Walker→Q03
skull (acquired)
congenital
with
hydrocephalus→Q03
Degeneration, degenerative1 unique routes
brain (cortical) (progressive)
in
congenital hydrocephalus→Q03
Distortion (s) (congenital)1 unique routes
skull bone (s) NEC
with
hydrocephalus→Q03
Hydrocephalus (acquired) (external) (internal) (malignant) (recurrent)5 unique routes
aqueduct Sylvius stricture→Q03
congenital (external) (internal)→Q03(2 variants)
specified NEC→Q03
foramen Magendie block (acquired)
congenital→Q03
newborn→Q03
Hypoplasia, hypoplastic1 unique routes
skull (bone)
with
hydrocephalus→Q03
Imperfect1 unique routes
closure (congenital)
skull
with
hydrocephalus→Q03
Obstruction, obstructed, obstructive2 unique routes
aqueduct of Sylvius
congenital→Q03
foramen of Monro (congenital)→Q03
Occlusion, occluded1 unique routes
aqueduct of Sylvius
congenital→Q03

MS-DRG Classification

2026

No direct MS-DRG triggers identified.

Cross Reference

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