Q03.0

Billable
ChapterQ00–Q99
Ranksubcategory
Official Description

Malformations of aqueduct of Sylvius

Metadata & Insights
  • •2026 ICD-10-CM Edition - Effective October 1, 2025.
  • •Billable/specific code (valid for reimbursement).
  • •Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (Q00-Q99).

Instructional Notes

Includes
  • Anomaly of aqueduct of Sylvius
  • Obstruction of aqueduct of Sylvius, congenital
  • Stenosis of aqueduct of Sylvius
General instructions are available for the parent sections:
View CH17 NotesView Q03 Notes

Clinical Hierarchy

CH17Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0)
Q00-Q07Congenital malformations of the nervous system (Q00-Q07)
Q03Congenital hydrocephalus
Q03.0Malformations of aqueduct of Sylvius

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to Q03.0:

categoryQ03
Congenital hydrocephalus
View context instructions
chapterCH17
Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0)
View context instructions

Alphabetic Index Mentions

These are Diagnosis Index lookup paths that route to Q03.0. Use them as entry terms for search, then confirm final coding instructions in the Tabular List and notes above.

8 raw paths
Anomaly, anomalous (congenital) (unspecified type)1 unique routes
aqueduct of Sylvius→Q03.0
Atresia, atretic1 unique routes
aqueduct of Sylvius→Q03.0
Hydrocephalus (acquired) (external) (internal) (malignant) (recurrent)1 unique routes
aqueduct Sylvius stricture→Q03.0
Obstruction, obstructed, obstructive1 unique routes
aqueduct of Sylvius
congenital→Q03.0
Occlusion, occluded1 unique routes
aqueduct of Sylvius
congenital→Q03.0
Septum, septate (congenital)1 unique routes
aqueduct of Sylvius→Q03.0
Stenosis, stenotic (cicatricial)1 unique routes
aqueduct of Sylvius (congenital)→Q03.0
Stricture1 unique routes
aqueduct of Sylvius (congenital)→Q03.0

MS-DRG Classification

2026 v43.1

This code is grouped within the following Diagnosis Related Group(s) for clinical reimbursement:

DRG 091
Other Disorders of Nervous System with MCC
DRG 092
Other Disorders of Nervous System with CC
DRG 093
Other Disorders of Nervous System without CC/MCC
DRG 791
Prematurity with Major Problems
DRG 793
Full Term Neonate with Major Problems

Cross Reference

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