Chapter 2

C00–D49: Neoplasms

Neoplasms diagnostic classification updated for 2026.

Internal Codes
  • C86.5|

    Angioimmunoblastic T-cell lymphoma

  • C86.50|

    Angioimmunoblastic T-cell lymphoma not having achieved remission

  • C86.51|

    Angioimmunoblastic T-cell lymphoma, in remission

  • C86.6|

    Primary cutaneous CD30-positive T-cell proliferations

  • C86.60|

    Primary cutaneous CD30-positive T-cell proliferations not having achieved remission

  • C86.61|

    Primary cutaneous CD30-positive T-cell proliferations, in remission

  • C88|

    Malignant immunoproliferative diseases and certain other B-cell lymphomas

  • C88.0|

    Waldenström macroglobulinemia

  • C88.00|

    Waldenström macroglobulinemia not having achieved remission

  • C88.01|

    Waldenström macroglobulinemia, in remission

  • C88.2|

    Heavy chain disease

  • C88.20|

    Heavy chain disease not having achieved remission

  • C88.21|

    Heavy chain disease, in remission

  • C88.3|

    Immunoproliferative small intestinal disease

  • C88.30|

    Immunoproliferative small intestinal disease not having achieved remission

  • C88.31|

    Immunoproliferative small intestinal disease, in remission

  • C88.4|

    Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma]

  • C88.40|

    Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma] not having achieved remission

  • C88.41|

    Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma], in remission

  • C88.8|

    Other malignant immunoproliferative diseases

  • C88.80|

    Other malignant immunoproliferative diseases not having achieved remission

  • C88.81|

    Other malignant immunoproliferative diseases, in remission

  • C88.9|

    Malignant immunoproliferative disease, unspecified

  • C88.90|

    Malignant immunoproliferative disease, unspecified not having achieved remission

  • C88.91|

    Malignant immunoproliferative disease, unspecified, in remission

  • C90|

    Multiple myeloma and malignant plasma cell neoplasms

  • C90.0|

    Multiple myeloma

  • C90.00|

    Multiple myeloma not having achieved remission

  • C90.01|

    Multiple myeloma in remission

  • C90.02|

    Multiple myeloma in relapse

  • C90.1|

    Plasma cell leukemia

  • C90.10|

    Plasma cell leukemia not having achieved remission

  • C90.11|

    Plasma cell leukemia in remission

  • C90.12|

    Plasma cell leukemia in relapse

  • C90.2|

    Extramedullary plasmacytoma

  • C90.20|

    Extramedullary plasmacytoma not having achieved remission

  • C90.21|

    Extramedullary plasmacytoma in remission

  • C90.22|

    Extramedullary plasmacytoma in relapse

  • C90.3|

    Solitary plasmacytoma

  • C90.30|

    Solitary plasmacytoma not having achieved remission

  • C90.31|

    Solitary plasmacytoma in remission

  • C90.32|

    Solitary plasmacytoma in relapse

  • C91|

    Lymphoid leukemia

  • C91.0|

    Acute lymphoblastic leukemia [ALL]

  • C91.00|

    Acute lymphoblastic leukemia not having achieved remission

  • C91.01|

    Acute lymphoblastic leukemia, in remission

  • C91.02|

    Acute lymphoblastic leukemia, in relapse

  • C91.1|

    Chronic lymphocytic leukemia of B-cell type

  • C91.10|

    Chronic lymphocytic leukemia of B-cell type not having achieved remission

  • C91.11|

    Chronic lymphocytic leukemia of B-cell type in remission

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