Chapter 2

C00–D49: Neoplasms

Neoplasms diagnostic classification updated for 2026.

Internal Codes
  • C86.5

    Angioimmunoblastic T-cell lymphoma

  • C86.50

    Angioimmunoblastic T-cell lymphoma not having achieved remission

  • C86.51

    Angioimmunoblastic T-cell lymphoma, in remission

  • C86.6

    Primary cutaneous CD30-positive T-cell proliferations

  • C86.60

    Primary cutaneous CD30-positive T-cell proliferations not having achieved remission

  • C86.61

    Primary cutaneous CD30-positive T-cell proliferations, in remission

  • C88

    Malignant immunoproliferative diseases and certain other B-cell lymphomas

  • C88.0

    Waldenström macroglobulinemia

  • C88.00

    Waldenström macroglobulinemia not having achieved remission

  • C88.01

    Waldenström macroglobulinemia, in remission

  • C88.2

    Heavy chain disease

  • C88.20

    Heavy chain disease not having achieved remission

  • C88.21

    Heavy chain disease, in remission

  • C88.3

    Immunoproliferative small intestinal disease

  • C88.30

    Immunoproliferative small intestinal disease not having achieved remission

  • C88.31

    Immunoproliferative small intestinal disease, in remission

  • C88.4

    Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma]

  • C88.40

    Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma] not having achieved remission

  • C88.41

    Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma], in remission

  • C88.8

    Other malignant immunoproliferative diseases

  • C88.80

    Other malignant immunoproliferative diseases not having achieved remission

  • C88.81

    Other malignant immunoproliferative diseases, in remission

  • C88.9

    Malignant immunoproliferative disease, unspecified

  • C88.90

    Malignant immunoproliferative disease, unspecified not having achieved remission

  • C88.91

    Malignant immunoproliferative disease, unspecified, in remission

  • C90

    Multiple myeloma and malignant plasma cell neoplasms

  • C90.0

    Multiple myeloma

  • C90.00

    Multiple myeloma not having achieved remission

  • C90.01

    Multiple myeloma in remission

  • C90.02

    Multiple myeloma in relapse

  • C90.1

    Plasma cell leukemia

  • C90.10

    Plasma cell leukemia not having achieved remission

  • C90.11

    Plasma cell leukemia in remission

  • C90.12

    Plasma cell leukemia in relapse

  • C90.2

    Extramedullary plasmacytoma

  • C90.20

    Extramedullary plasmacytoma not having achieved remission

  • C90.21

    Extramedullary plasmacytoma in remission

  • C90.22

    Extramedullary plasmacytoma in relapse

  • C90.3

    Solitary plasmacytoma

  • C90.30

    Solitary plasmacytoma not having achieved remission

  • C90.31

    Solitary plasmacytoma in remission

  • C90.32

    Solitary plasmacytoma in relapse

  • C91

    Lymphoid leukemia

  • C91.0

    Acute lymphoblastic leukemia [ALL]

  • C91.00

    Acute lymphoblastic leukemia not having achieved remission

  • C91.01

    Acute lymphoblastic leukemia, in remission

  • C91.02

    Acute lymphoblastic leukemia, in relapse

  • C91.1

    Chronic lymphocytic leukemia of B-cell type

  • C91.10

    Chronic lymphocytic leukemia of B-cell type not having achieved remission

  • C91.11

    Chronic lymphocytic leukemia of B-cell type in remission

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