Chapter 1

A00–B99: Certain Infectious and Parasitic Diseases

Certain Infectious and Parasitic Diseases diagnostic classification updated for 2026.

Chapter Instructions

Includes
  • diseases generally recognized as communicable or transmissible
Excludes1(Not coded here. Use a different code.)
  • certain localized infections - see body system-related chapters
Excludes2(Not included here. Code separately if applicable.)
  • carrier or suspected carrier of infectious disease (Z22.-)
  • infectious and parasitic diseases complicating pregnancy, childbirth and the puerperium (O98.-)
  • infectious and parasitic diseases specific to the perinatal period (P35-P39)
  • influenza and other acute respiratory infections (J00-J22)
Use Additional Code
  • code to identify resistance to antimicrobial drugs (Z16.-)
Internal Codes
  • A49.02

    Methicillin resistant Staphylococcus aureus infection, unspecified site

  • A49.1

    Streptococcal infection, unspecified site

  • A49.2

    Hemophilus influenzae infection, unspecified site

  • A49.3

    Mycoplasma infection, unspecified site

  • A49.8

    Other bacterial infections of unspecified site

  • A49.9

    Bacterial infection, unspecified

  • A50

    Congenital syphilis

  • A50.0

    Early congenital syphilis, symptomatic

  • A50.01

    Early congenital syphilitic oculopathy

  • A50.02

    Early congenital syphilitic osteochondropathy

  • A50.03

    Early congenital syphilitic pharyngitis

  • A50.04

    Early congenital syphilitic pneumonia

  • A50.05

    Early congenital syphilitic rhinitis

  • A50.06

    Early cutaneous congenital syphilis

  • A50.07

    Early mucocutaneous congenital syphilis

  • A50.08

    Early visceral congenital syphilis

  • A50.09

    Other early congenital syphilis, symptomatic

  • A50.1

    Early congenital syphilis, latent

  • A50.2

    Early congenital syphilis, unspecified

  • A50.3

    Late congenital syphilitic oculopathy

  • A50.30

    Late congenital syphilitic oculopathy, unspecified

  • A50.31

    Late congenital syphilitic interstitial keratitis

  • A50.32

    Late congenital syphilitic chorioretinitis

  • A50.39

    Other late congenital syphilitic oculopathy

  • A50.4

    Late congenital neurosyphilis [juvenile neurosyphilis]

  • A50.40

    Late congenital neurosyphilis, unspecified

  • A50.41

    Late congenital syphilitic meningitis

  • A50.42

    Late congenital syphilitic encephalitis

  • A50.43

    Late congenital syphilitic polyneuropathy

  • A50.44

    Late congenital syphilitic optic nerve atrophy

  • A50.45

    Juvenile general paresis

  • A50.49

    Other late congenital neurosyphilis

  • A50.5

    Other late congenital syphilis, symptomatic

  • A50.51

    Clutton's joints

  • A50.52

    Hutchinson's teeth

  • A50.53

    Hutchinson's triad

  • A50.54

    Late congenital cardiovascular syphilis

  • A50.55

    Late congenital syphilitic arthropathy

  • A50.56

    Late congenital syphilitic osteochondropathy

  • A50.57

    Syphilitic saddle nose

  • A50.59

    Other late congenital syphilis, symptomatic

  • A50.6

    Late congenital syphilis, latent

  • A50.7

    Late congenital syphilis, unspecified

  • A50.9

    Congenital syphilis, unspecified

  • A51

    Early syphilis

  • A51.0

    Primary genital syphilis

  • A51.1

    Primary anal syphilis

  • A51.2

    Primary syphilis of other sites

  • A51.3

    Secondary syphilis of skin and mucous membranes

  • A51.31

    Condyloma latum

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