Lynch syndrome
Congenital Malformations, Deformations and Chromosomal Abnormalities·Inherited neoplasm predisposition syndromes involving multiple systems, not elsewhere classified·subcategory·FY 2027
Also indexed as: Susceptibility to disease, hereditary nonpolyposis colorectal cancer; Syndrome, Lynch
Instructional notes
Includes: conditions that are coded here
- Hereditary nonpolyposis colorectal cancer susceptibility
- Lynch syndrome due to EPCAM
- Lynch syndrome due to MLH1
- Lynch syndrome due to MSH2
- Lynch syndrome due to MSH6
- Lynch syndrome due to PMS2
Also applies, from QA1: Genetic disorders associated with neoplasms, not elsewhere classified
These notes sit on QA1 and apply to every code under it, including QA1.71.
Excludes2: not included here, code separately if applicable
- multiple endocrine neoplasia [MEN] syndromes (E31.2-)
Code also: add a code for this too, order depends on the encounter
- if applicable, any associated conditions, such as:
- genetic susceptibility to malignant neoplasm by site (Z15.0-)
- malignant neoplasms (C00.0-C96.9)
- personal history of malignant neoplasm (Z85.-)
Where QA1.71 sits
MS-DRGs
As the principal diagnosis, this code groups to these MS-DRGs (v44.0).
Code history
- FY 2026: replaced Z15.09 (Genetic susceptibility to other malignant neoplasm)