All ICD10 Codes

N01

Non-Billable
ChapterN00–N99
Rankcategory
Official Description

Rapidly progressive nephritic syndrome

Use a more specific code (11 billable)
N01.0Rapidly progressive nephritic syndrome with minor glomerular abnormalityN01.1Rapidly progressive nephritic syndrome with focal and segmental glomerular lesionsN01.2Rapidly progressive nephritic syndrome with diffuse membranous glomerulonephritisN01.3Rapidly progressive nephritic syndrome with diffuse mesangial proliferative glomerulonephritisN01.4Rapidly progressive nephritic syndrome with diffuse endocapillary proliferative glomerulonephritisN01.5Rapidly progressive nephritic syndrome with diffuse mesangiocapillary glomerulonephritisN01.6Rapidly progressive nephritic syndrome with dense deposit diseaseN01.7Rapidly progressive nephritic syndrome with diffuse crescentic glomerulonephritisN01.8Rapidly progressive nephritic syndrome with other morphologic changesN01.9Rapidly progressive nephritic syndrome with unspecified morphologic changesN01.ARapidly progressive nephritic syndrome with C3 glomerulonephritis
Metadata & Insights
  • •Non-billable category (requires more specific sub-code).
  • •Chapter 14: Diseases of the Genitourinary System (N00-N99).

CH14 Parent Instructions

Excludes2(Not included here. Code separately if applicable.)
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)

N00-N08 Parent Instructions

Excludes1(Not coded here. Use a different code.)
  • hypertensive chronic kidney disease (I12.-)
Code Also
  • any associated kidney failure (N17-N19).

Instructional Notes

Includes
  • rapidly progressive glomerular disease
  • rapidly progressive glomerulonephritis
  • rapidly progressive nephritis
Excludes1(Not coded here. Use a different code.)
  • nephritic syndrome NOS (N05.-)

Clinical Hierarchy

BillableHas subcodes
CH14Diseases of the genitourinary system (N00-N99)
N00-N08Glomerular diseases (N00-N08)
N01Rapidly progressive nephritic syndromeNot billable
N01.0Rapidly progressive nephritic syndrome with minor glomerular abnormalityBillable
N01.1Rapidly progressive nephritic syndrome with focal and segmental glomerular lesionsBillable
N01.2Rapidly progressive nephritic syndrome with diffuse membranous glomerulonephritisBillable
N01.3Rapidly progressive nephritic syndrome with diffuse mesangial proliferative glomerulonephritisBillable
N01.4Rapidly progressive nephritic syndrome with diffuse endocapillary proliferative glomerulonephritisBillable
N01.5Rapidly progressive nephritic syndrome with diffuse mesangiocapillary glomerulonephritisBillable
N01.6Rapidly progressive nephritic syndrome with dense deposit diseaseBillable
N01.7Rapidly progressive nephritic syndrome with diffuse crescentic glomerulonephritisBillable
N01.8Rapidly progressive nephritic syndrome with other morphologic changesBillable
N01.9Rapidly progressive nephritic syndrome with unspecified morphologic changesBillable
N01.ARapidly progressive nephritic syndrome with C3 glomerulonephritisBillable

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to N01:

blockN00-N08
Glomerular diseases (N00-N08)
View context instructions
chapterCH14
Diseases of the genitourinary system (N00-N99)
View context instructions

MS-DRG Classification

2026

No direct MS-DRG triggers identified.

Cross Reference

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