Chapter 10

J00–J99: Diseases of the Respiratory System

Diseases of the Respiratory System diagnostic classification updated for 2026.

Chapter Instructions

Excludes2(Not included here. Code separately if applicable.)
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • smoke inhalation (T59.81-)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Use Additional Code
  • code, where applicable, to identify:
  • exposure to environmental tobacco smoke (Z77.22)
  • exposure to tobacco smoke in the perinatal period (P96.81)
  • history of tobacco dependence (Z87.891)
  • occupational exposure to environmental tobacco smoke (Z57.31)
  • tobacco dependence (F17.-)
  • tobacco use (Z72.0)
Internal Codes
  • J81.0

    Acute pulmonary edema

  • J81.1

    Chronic pulmonary edema

  • J82.81

    Chronic eosinophilic pneumonia

  • J82.82

    Acute eosinophilic pneumonia

  • J82.83

    Eosinophilic asthma

  • J82.89

    Other pulmonary eosinophilia, not elsewhere classified

  • J84.01

    Alveolar proteinosis

  • J84.02

    Pulmonary alveolar microlithiasis

  • J84.03

    Idiopathic pulmonary hemosiderosis

  • J84.09

    Other alveolar and parieto-alveolar conditions

  • J84.10

    Pulmonary fibrosis, unspecified

  • J84.111

    Idiopathic interstitial pneumonia, not otherwise specified

  • J84.112

    Idiopathic pulmonary fibrosis

  • J84.113

    Idiopathic non-specific interstitial pneumonitis

  • J84.114

    Acute interstitial pneumonitis

  • J84.115

    Respiratory bronchiolitis interstitial lung disease

  • J84.116

    Cryptogenic organizing pneumonia

  • J84.117

    Desquamative interstitial pneumonia

  • J84.170

    Interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere

  • J84.178

    Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere

  • J84.2

    Lymphoid interstitial pneumonia

  • J84.81

    Lymphangioleiomyomatosis

  • J84.82

    Adult pulmonary Langerhans cell histiocytosis

  • J84.83

    Surfactant mutations of the lung

  • J84.841

    Neuroendocrine cell hyperplasia of infancy

  • J84.842

    Pulmonary interstitial glycogenosis

  • J84.843

    Alveolar capillary dysplasia with vein misalignment

  • J84.848

    Other interstitial lung diseases of childhood

  • J84.89

    Other specified interstitial pulmonary diseases

  • J84.9

    Interstitial pulmonary disease, unspecified

  • J85.0

    Gangrene and necrosis of lung

  • J85.1

    Abscess of lung with pneumonia

  • J85.2

    Abscess of lung without pneumonia

  • J85.3

    Abscess of mediastinum

  • J86.0

    Pyothorax with fistula

  • J86.9

    Pyothorax without fistula

  • J90

    Pleural effusion, not elsewhere classified

  • J91.0

    Malignant pleural effusion

  • J91.8

    Pleural effusion in other conditions classified elsewhere

  • J92.0

    Pleural plaque with presence of asbestos

  • J92.9

    Pleural plaque without asbestos

  • J93.0

    Spontaneous tension pneumothorax

  • J93.11

    Primary spontaneous pneumothorax

  • J93.12

    Secondary spontaneous pneumothorax

  • J93.81

    Chronic pneumothorax

  • J93.82

    Other air leak

  • J93.83

    Other pneumothorax

  • J93.9

    Pneumothorax, unspecified

  • J94.0

    Chylous effusion

  • J94.1

    Fibrothorax

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