I00Billable, valid for claims from October 1, 2026

Rheumatic fever without heart involvement

In Acute rheumatic fever (I00-I02), chapter 9: Diseases of the Circulatory System

  • I00 is billable and valid on claims for FY 2027. If the record has more detail, check the other codes under I00-I02 below.
  • As a secondary diagnosis it is not a CC or MCC, so it doesn't raise the MS-DRG payment.
  • Doesn't count toward a Medicare Advantage risk score (no HCC in V28).
  • AHRQ's Chronic Condition Indicator classes it as not chronic (an acute or short-term condition).

Also indexed as: Erythema, marginatum, in acute rheumatic fever; Fever, rheumatic; Pneumonia, in, rheumatic fever; Pneumonia, rheumatic; Rheumatic, pneumonia

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Instructional notes

Includes: conditions that are coded here

  • arthritis, rheumatic, acute or subacute

Excludes1: not coded here, use a different code

  • rheumatic fever with heart involvement (I01.0 -I01.9)

Official coding guidelines

From the ICD-10-CM Official Guidelines for Coding and Reporting, FY 2027 (CMS and NCHS). Links open the PDF at the right page.

Covers hypertension with heart and kidney disease, coronary artery disease with angina, perioperative stroke, cerebrovascular sequelae, and acute myocardial infarction types and timing.

Read Section I.C.9 (page 50)

Other codes under I00-I02

Acute rheumatic fever (I00-I02)

I00 MS-DRGs

As the principal diagnosis, I00 groups to MS-DRG 545, 546, or 547 (v44.0). Which one applies depends on procedures performed, secondary diagnoses (CC/MCC), and the patient's age and discharge status.

Related conditions

Grouped by AHRQ's Clinical Classifications Software Refined (CCSR), which sorts every diagnosis code into clinically meaningful categories.

I00 is in Acute rheumatic heart disease (CIR002, its default category), with 8 codes. Others in it:

  • I01.0 Acute rheumatic pericarditis
  • I01.1 Acute rheumatic endocarditis
  • I01.2 Acute rheumatic myocarditis
  • I01.8 Other acute rheumatic heart disease
  • I01.9 Acute rheumatic heart disease, unspecified
  • I02.0 Rheumatic chorea with heart involvement
  • I02.9 Rheumatic chorea without heart involvement

I00 is in Bacterial infections (INF003), with 398 codes. Others in it:

  • A00.0 Cholera due to Vibrio cholerae 01, biovar cholerae
  • A00.1 Cholera due to Vibrio cholerae 01, biovar eltor
  • A00.9 Cholera, unspecified
  • A01.00 Typhoid fever, unspecified
  • A01.01 Typhoid meningitis
  • A01.02 Typhoid fever with heart involvement
  • A01.03 Typhoid pneumonia
  • A01.04 Typhoid arthritis

Medicare coverage articles listing I00

This Medicare billing and coding article lists I00 as a diagnosis that supports medical necessity for the services they cover. From the CMS Medicare Coverage Database; check your own contractor's article before billing.

Other codes that refer to I00

Notes on these codes point to I00.

  • I01.0 Includes: Any condition in I00 with pericarditis
  • I01.1 Includes: Any condition in I00 with endocarditis or valvulitis
  • I01.2 Includes: Any condition in I00 with myocarditis
  • I01.8 Includes: Any condition in I00 with other or multiple types of heart involvement
  • I01.9 Includes: Any condition in I00 with unspecified type of heart involvement
  • I51 Excludes2: heart disease specified as rheumatic (I00-I09)
  • J09-J18 Excludes2: rheumatic pneumonia (I00)
  • J17 Code First: rheumatic fever (I00)
  • M02 Excludes1: rheumatic fever (I00)
  • M05 Excludes1: rheumatic fever (I00)
  • O99.4 Includes: Conditions in I00-I99
  • P00.3 Includes: Newborn affected by maternal conditions classifiable to I00-I99, J00-J99, Q20-Q34 and not included in P00.0, P00.2
  • Z82.4 Includes: Conditions classifiable to I00-I5A, I65-I99
  • Z86.7 Includes: Conditions classifiable to I00-I99

About the condition

Plain-language background from MedlinePlus (National Library of Medicine), not coding guidance.

Streptococcal Infections

Strep is short for Streptococcus, a type of bacteria that often lives in your nose and throat. Most strep infections are mild, but some may become serious depending on your overall health.

Read more about streptococcal infections on MedlinePlus

Code history

Valid since FY2016, when ICD-10-CM took effect on October 1, 2015. No changes since.

ICD-9-CM equivalent

Legacy crosswalk from the CMS General Equivalence Mappings (last updated 2018).

  • 390 Rheumatic fever without mention of heart involvement
ICD-9 to ICD-10 converter