Chapter 7

H00–H59: Diseases of the Eye and Adnexa

Diseases of the Eye and Adnexa diagnostic classification updated for 2026.

Chapter Instructions

Excludes2(Not included here. Code separately if applicable.)
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
  • diabetes mellitus related eye conditions (E09.3-, E10.3-, E11.3-, E13.3-)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury (trauma) of eye and orbit (S05.-)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
  • syphilis related eye disorders (A50.01, A50.3-, A51.43, A52.71)
Internal Codes
  • H47.321

    Drusen of optic disc, right eye

  • H47.322

    Drusen of optic disc, left eye

  • H47.323

    Drusen of optic disc, bilateral

  • H47.329

    Drusen of optic disc, unspecified eye

  • H47.33

    Pseudopapilledema of optic disc

  • H47.331

    Pseudopapilledema of optic disc, right eye

  • H47.332

    Pseudopapilledema of optic disc, left eye

  • H47.333

    Pseudopapilledema of optic disc, bilateral

  • H47.339

    Pseudopapilledema of optic disc, unspecified eye

  • H47.39

    Other disorders of optic disc

  • H47.391

    Other disorders of optic disc, right eye

  • H47.392

    Other disorders of optic disc, left eye

  • H47.393

    Other disorders of optic disc, bilateral

  • H47.399

    Other disorders of optic disc, unspecified eye

  • H47.4

    Disorders of optic chiasm

  • H47.41

    Disorders of optic chiasm in (due to) inflammatory disorders

  • H47.42

    Disorders of optic chiasm in (due to) neoplasm

  • H47.43

    Disorders of optic chiasm in (due to) vascular disorders

  • H47.49

    Disorders of optic chiasm in (due to) other disorders

  • H47.5

    Disorders of other visual pathways

  • H47.51

    Disorders of visual pathways in (due to) inflammatory disorders

  • H47.511

    Disorders of visual pathways in (due to) inflammatory disorders, right side

  • H47.512

    Disorders of visual pathways in (due to) inflammatory disorders, left side

  • H47.519

    Disorders of visual pathways in (due to) inflammatory disorders, unspecified side

  • H47.52

    Disorders of visual pathways in (due to) neoplasm

  • H47.521

    Disorders of visual pathways in (due to) neoplasm, right side

  • H47.522

    Disorders of visual pathways in (due to) neoplasm, left side

  • H47.529

    Disorders of visual pathways in (due to) neoplasm, unspecified side

  • H47.53

    Disorders of visual pathways in (due to) vascular disorders

  • H47.531

    Disorders of visual pathways in (due to) vascular disorders, right side

  • H47.532

    Disorders of visual pathways in (due to) vascular disorders, left side

  • H47.539

    Disorders of visual pathways in (due to) vascular disorders, unspecified side

  • H47.6

    Disorders of visual cortex

  • H47.61

    Cortical blindness

  • H47.611

    Cortical blindness, right side of brain

  • H47.612

    Cortical blindness, left side of brain

  • H47.619

    Cortical blindness, unspecified side of brain

  • H47.62

    Disorders of visual cortex in (due to) inflammatory disorders

  • H47.621

    Disorders of visual cortex in (due to) inflammatory disorders, right side of brain

  • H47.622

    Disorders of visual cortex in (due to) inflammatory disorders, left side of brain

  • H47.629

    Disorders of visual cortex in (due to) inflammatory disorders, unspecified side of brain

  • H47.63

    Disorders of visual cortex in (due to) neoplasm

  • H47.631

    Disorders of visual cortex in (due to) neoplasm, right side of brain

  • H47.632

    Disorders of visual cortex in (due to) neoplasm, left side of brain

  • H47.639

    Disorders of visual cortex in (due to) neoplasm, unspecified side of brain

  • H47.64

    Disorders of visual cortex in (due to) vascular disorders

  • H47.641

    Disorders of visual cortex in (due to) vascular disorders, right side of brain

  • H47.642

    Disorders of visual cortex in (due to) vascular disorders, left side of brain

  • H47.649

    Disorders of visual cortex in (due to) vascular disorders, unspecified side of brain

  • H47.9

    Unspecified disorder of visual pathways

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