Chapter 7

H00–H59: Diseases of the Eye and Adnexa

Diseases of the Eye and Adnexa diagnostic classification updated for 2026.

Chapter Instructions

Excludes2(Not included here. Code separately if applicable.)
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
  • diabetes mellitus related eye conditions (E09.3-, E10.3-, E11.3-, E13.3-)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury (trauma) of eye and orbit (S05.-)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
  • syphilis related eye disorders (A50.01, A50.3-, A51.43, A52.71)
Internal Codes
  • H54.1141

    Blindness right eye category 4, low vision left eye category 1

  • H54.1142

    Blindness right eye category 4, low vision left eye category 2

  • H54.1151

    Blindness right eye category 5, low vision left eye category 1

  • H54.1152

    Blindness right eye category 5, low vision left eye category 2

  • H54.1213

    Low vision right eye category 1, blindness left eye category 3

  • H54.1214

    Low vision right eye category 1, blindness left eye category 4

  • H54.1215

    Low vision right eye category 1, blindness left eye category 5

  • H54.1223

    Low vision right eye category 2, blindness left eye category 3

  • H54.1224

    Low vision right eye category 2, blindness left eye category 4

  • H54.1225

    Low vision right eye category 2, blindness left eye category 5

  • H54.2X11

    Low vision right eye category 1, low vision left eye category 1

  • H54.2X12

    Low vision right eye category 1, low vision left eye category 2

  • H54.2X21

    Low vision right eye category 2, low vision left eye category 1

  • H54.2X22

    Low vision right eye category 2, low vision left eye category 2

  • H54.3

    Unqualified visual loss, both eyes

  • H54.40

    Blindness, one eye, unspecified eye

  • H54.413A

    Blindness right eye category 3, normal vision left eye

  • H54.414A

    Blindness right eye category 4, normal vision left eye

  • H54.415A

    Blindness right eye category 5, normal vision left eye

  • H54.42A3

    Blindness left eye category 3, normal vision right eye

  • H54.42A4

    Blindness left eye category 4, normal vision right eye

  • H54.42A5

    Blindness left eye category 5, normal vision right eye

  • H54.50

    Low vision, one eye, unspecified eye

  • H54.511A

    Low vision right eye category 1, normal vision left eye

  • H54.512A

    Low vision right eye category 2, normal vision left eye

  • H54.52A1

    Low vision left eye category 1, normal vision right eye

  • H54.52A2

    Low vision left eye category 2, normal vision right eye

  • H54.60

    Unqualified visual loss, one eye, unspecified

  • H54.61

    Unqualified visual loss, right eye, normal vision left eye

  • H54.62

    Unqualified visual loss, left eye, normal vision right eye

  • H54.7

    Unspecified visual loss

  • H54.8

    Legal blindness, as defined in USA

  • H55.00

    Unspecified nystagmus

  • H55.01

    Congenital nystagmus

  • H55.02

    Latent nystagmus

  • H55.03

    Visual deprivation nystagmus

  • H55.04

    Dissociated nystagmus

  • H55.09

    Other forms of nystagmus

  • H55.81

    Deficient saccadic eye movements

  • H55.82

    Deficient smooth pursuit eye movements

  • H55.89

    Other irregular eye movements

  • H57.00

    Unspecified anomaly of pupillary function

  • H57.01

    Argyll Robertson pupil, atypical

  • H57.02

    Anisocoria

  • H57.03

    Miosis

  • H57.04

    Mydriasis

  • H57.051

    Tonic pupil, right eye

  • H57.052

    Tonic pupil, left eye

  • H57.053

    Tonic pupil, bilateral

  • H57.059

    Tonic pupil, unspecified eye

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