Chapter 6

G00–G99: Diseases of the Nervous System

Diseases of the Nervous System diagnostic classification updated for 2026.

Chapter Instructions

Excludes2(Not included here. Code separately if applicable.)
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Internal Codes
  • G62.9

    Polyneuropathy, unspecified

  • G63

    Polyneuropathy in diseases classified elsewhere

  • G64

    Other disorders of peripheral nervous system

  • G65

    Sequelae of inflammatory and toxic polyneuropathies

  • G65.0

    Sequelae of Guillain-Barré syndrome

  • G65.1

    Sequelae of other inflammatory polyneuropathy

  • G65.2

    Sequelae of toxic polyneuropathy

  • G70

    Myasthenia gravis and other myoneural disorders

  • G70.0

    Myasthenia gravis

  • G70.00

    Myasthenia gravis without (acute) exacerbation

  • G70.01

    Myasthenia gravis with (acute) exacerbation

  • G70.1

    Toxic myoneural disorders

  • G70.2

    Congenital and developmental myasthenia

  • G70.8

    Other specified myoneural disorders

  • G70.80

    Lambert-Eaton syndrome, unspecified

  • G70.81

    Lambert-Eaton syndrome in disease classified elsewhere

  • G70.89

    Other specified myoneural disorders

  • G70.9

    Myoneural disorder, unspecified

  • G71

    Primary disorders of muscles

  • G71.0

    Muscular dystrophy

  • G71.00

    Muscular dystrophy, unspecified

  • G71.01

    Duchenne or Becker muscular dystrophy

  • G71.02

    Facioscapulohumeral muscular dystrophy

  • G71.03

    Limb girdle muscular dystrophies

  • G71.031

    Autosomal dominant limb girdle muscular dystrophy

  • G71.032

    Autosomal recessive limb girdle muscular dystrophy due to calpain-3 dysfunction

  • G71.033

    Limb girdle muscular dystrophy due to dysferlin dysfunction

  • G71.034

    Limb girdle muscular dystrophy due to sarcoglycan dysfunction

  • G71.0340

    Limb girdle muscular dystrophy due to sarcoglycan dysfunction, unspecified

  • G71.0341

    Limb girdle muscular dystrophy due to alpha sarcoglycan dysfunction

  • G71.0342

    Limb girdle muscular dystrophy due to beta sarcoglycan dysfunction

  • G71.0349

    Limb girdle muscular dystrophy due to other sarcoglycan dysfunction

  • G71.035

    Limb girdle muscular dystrophy due to anoctamin-5 dysfunction

  • G71.036

    Limb girdle muscular dystrophy due to fukutin related protein dysfunction

  • G71.038

    Other limb girdle muscular dystrophy

  • G71.039

    Limb girdle muscular dystrophy, unspecified

  • G71.09

    Other specified muscular dystrophies

  • G71.1

    Myotonic disorders

  • G71.11

    Myotonic muscular dystrophy

  • G71.12

    Myotonia congenita

  • G71.13

    Myotonic chondrodystrophy

  • G71.14

    Drug induced myotonia

  • G71.19

    Other specified myotonic disorders

  • G71.2

    Congenital myopathies

  • G71.20

    Congenital myopathy, unspecified

  • G71.21

    Nemaline myopathy

  • G71.22

    Centronuclear myopathy

  • G71.220

    X-linked myotubular myopathy

  • G71.228

    Other centronuclear myopathy

  • G71.29

    Other congenital myopathy

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