Chapter 6

G00–G99: Diseases of the Nervous System

Diseases of the Nervous System diagnostic classification updated for 2026.

Chapter Instructions

Excludes2(Not included here. Code separately if applicable.)
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Internal Codes
  • G90.1

    Familial dysautonomia [Riley-Day]

  • G90.2

    Horner's syndrome

  • G90.3

    Multi-system degeneration of the autonomic nervous system

  • G90.4

    Autonomic dysreflexia

  • G90.50

    Complex regional pain syndrome I, unspecified

  • G90.511

    Complex regional pain syndrome I of right upper limb

  • G90.512

    Complex regional pain syndrome I of left upper limb

  • G90.513

    Complex regional pain syndrome I of upper limb, bilateral

  • G90.519

    Complex regional pain syndrome I of unspecified upper limb

  • G90.521

    Complex regional pain syndrome I of right lower limb

  • G90.522

    Complex regional pain syndrome I of left lower limb

  • G90.523

    Complex regional pain syndrome I of lower limb, bilateral

  • G90.529

    Complex regional pain syndrome I of unspecified lower limb

  • G90.59

    Complex regional pain syndrome I of other specified site

  • G90.81

    Serotonin syndrome

  • G90.89

    Other disorders of autonomic nervous system

  • G90.9

    Disorder of the autonomic nervous system, unspecified

  • G90.A

    Postural orthostatic tachycardia syndrome [POTS]

  • G90.B

    LMNB1-related autosomal dominant leukodystrophy

  • G91.0

    Communicating hydrocephalus

  • G91.1

    Obstructive hydrocephalus

  • G91.2

    (Idiopathic) normal pressure hydrocephalus

  • G91.3

    Post-traumatic hydrocephalus, unspecified

  • G91.4

    Hydrocephalus in diseases classified elsewhere

  • G91.8

    Other hydrocephalus

  • G91.9

    Hydrocephalus, unspecified

  • G92.00

    Immune effector cell-associated neurotoxicity syndrome, grade unspecified

  • G92.01

    Immune effector cell-associated neurotoxicity syndrome, grade 1

  • G92.02

    Immune effector cell-associated neurotoxicity syndrome, grade 2

  • G92.03

    Immune effector cell-associated neurotoxicity syndrome, grade 3

  • G92.04

    Immune effector cell-associated neurotoxicity syndrome, grade 4

  • G92.05

    Immune effector cell-associated neurotoxicity syndrome, grade 5

  • G92.8

    Other toxic encephalopathy

  • G92.9

    Unspecified toxic encephalopathy

  • G93.0

    Cerebral cysts

  • G93.1

    Anoxic brain damage, not elsewhere classified

  • G93.2

    Benign intracranial hypertension

  • G93.31

    Postviral fatigue syndrome

  • G93.32

    Myalgic encephalomyelitis/chronic fatigue syndrome

  • G93.39

    Other post infection and related fatigue syndromes

  • G93.40

    Encephalopathy, unspecified

  • G93.41

    Metabolic encephalopathy

  • G93.42

    Megalencephalic leukoencephalopathy with subcortical cysts

  • G93.43

    Leukoencephalopathy with calcifications and cysts

  • G93.44

    Adult-onset leukodystrophy with axonal spheroids

  • G93.45

    Developmental and epileptic encephalopathy

  • G93.49

    Other encephalopathy

  • G93.5

    Compression of brain

  • G93.6

    Cerebral edema

  • G93.7

    Reye's syndrome

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