Huntington's disease
In Systemic atrophies primarily affecting the central nervous system (G10-G14), chapter 6: Diseases of the Nervous System
- G10 is billable and valid on claims for FY 2027. If the record has more detail, check the other codes under G10-G14 below.
- As a secondary diagnosis it is a CC (complication or comorbidity), which can raise the MS-DRG payment. It doesn't count when the principal diagnosis is one of 67 closely related codes.
- Counts toward HCC 200 (Friedreich and Other Hereditary Ataxias; Huntington Disease) in the Medicare Advantage risk model (CMS-HCC V28).
- AHRQ's Chronic Condition Indicator classes it as chronic: expected to last 12 months or longer and to limit daily life or need ongoing care.
- 1,214 US deaths in 2024 had an underlying cause in category G10, per the National Vital Statistics System on CDC WONDER. Death records use WHO ICD-10, so the count is for the whole category.
Also indexed as: Chorea, hereditary; Chorea, Huntington's; Chorea, progressive, hereditary; Dementia), in, Huntington's disease or chorea; Dementia), in, Huntington's disease or chorea, with behavioral disturbance; Disease, Huntington's; Disease, Huntington's, with dementia; Huntington's disease or chorea; Huntington's disease or chorea, with dementia; Huntington's disease or chorea, with dementia, with behavioral disturbance
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Instructional notes
Includes: conditions that are coded here
- Huntington's chorea
- Huntington's dementia
Use additional code: add a second code for this, listed after this one
- code, if applicable, to identify:
- dementia with anxiety (F02.84, F02.A4, F02.B4, F02.C4)
- dementia with behavioral disturbance (F02.81-, F02.A1-, F02.B1-, F02.C1-)
- dementia with mood disturbance (F02.83, F02.A3, F02.B3, F02.C3)
- dementia with psychotic disturbance (F02.82, F02.A2, F02.B2, F02.C2)
- dementia without behavioral disturbance (F02.80, F02.A0, F02.B0, F02.C0)
- mild neurocognitive disorder due to known physiological condition (F06.7-)
Official coding guidelines
From the ICD-10-CM Official Guidelines for Coding and Reporting, FY 2027 (CMS and NCHS). Links open the PDF at the right page.
Covers default dominant or nondominant side for hemiplegia and monoplegia, and use and sequencing of G89 pain codes, including postoperative, chronic, and neoplasm-related pain.
- Dominant/nondominant side (page 45)
- Pain - Category G89 (page 45)
Other codes under G10-G14
Systemic atrophies primarily affecting the central nervous system (G10-G14)
G10 MS-DRGs
As the principal diagnosis, G10 groups to MS-DRG 056 or 057 (v44.0). Which one applies depends on procedures performed, secondary diagnoses (CC/MCC), and the patient's age and discharge status.
Related conditions
Grouped by AHRQ's Clinical Classifications Software Refined (CCSR), which sorts every diagnosis code into clinically meaningful categories.
G10 is in Other nervous system disorders (often hereditary or degenerative) (NVS006, its default category), with 103 codes. Others in it:
Medicare coverage articles listing G10
These 11 Medicare billing and coding articles list G10 as a diagnosis that supports medical necessity for the services they cover. From the CMS Medicare Coverage Database; check your own contractor's article before billing.
- Pharmacogenomics Testing (2 contractors)
- CT of the Head
- Cognitive Assessment and Care Plan Service
- MRI and CT Scans of the Head and Neck
- Neurophysiology Evoked Potentials (NEPs)
- Outpatient Speech Language Pathology
- Pharmacogenomic Testing
- Psychiatric Codes
- Psychiatry and Psychology Services
- Speech Language Pathology (SLP) Services: Communication Disorders
And 1 more.
Other codes that refer to G10
Notes on these codes point to G10.
About the condition
Plain-language background from MedlinePlus (National Library of Medicine), not coding guidance.
Huntington's Disease
Huntington's disease (HD) is an inherited disease that causes certain nerve cells in the brain to waste away. People are born with the defective gene, but symptoms usually don't appear until middle age. Early symptoms of HD may include uncontrolled movements, clumsiness, and balance problems. Later, HD can take away the ability to walk, talk, and swallow. Some people stop recognizing family members. Others are aware of their environment and are able to express emotions.
Read more about huntington's disease on MedlinePlusCode history
Valid since FY2016, when ICD-10-CM took effect on October 1, 2015. No changes since.
ICD-9-CM equivalent
Legacy crosswalk from the CMS General Equivalence Mappings (last updated 2018).
- 333.4 Huntington's chorea