Chapter 4

E00–E89: Endocrine, Nutritional and Metabolic Diseases

Endocrine, Nutritional and Metabolic Diseases diagnostic classification updated for 2026.

Chapter Instructions

Excludes1(Not coded here. Use a different code.)
  • transitory endocrine and metabolic disorders specific to newborn (P70-P74)
Internal Codes
  • E00|

    Congenital iodine-deficiency syndrome

  • E00.0|

    Congenital iodine-deficiency syndrome, neurological type

  • E00.1|

    Congenital iodine-deficiency syndrome, myxedematous type

  • E00.2|

    Congenital iodine-deficiency syndrome, mixed type

  • E00.9|

    Congenital iodine-deficiency syndrome, unspecified

  • E01|

    Iodine-deficiency related thyroid disorders and allied conditions

  • E01.0|

    Iodine-deficiency related diffuse (endemic) goiter

  • E01.1|

    Iodine-deficiency related multinodular (endemic) goiter

  • E01.2|

    Iodine-deficiency related (endemic) goiter, unspecified

  • E01.8|

    Other iodine-deficiency related thyroid disorders and allied conditions

  • E02|

    Subclinical iodine-deficiency hypothyroidism

  • E03|

    Other hypothyroidism

  • E03.0|

    Congenital hypothyroidism with diffuse goiter

  • E03.1|

    Congenital hypothyroidism without goiter

  • E03.2|

    Hypothyroidism due to medicaments and other exogenous substances

  • E03.3|

    Postinfectious hypothyroidism

  • E03.4|

    Atrophy of thyroid (acquired)

  • E03.5|

    Myxedema coma

  • E03.8|

    Other specified hypothyroidism

  • E03.9|

    Hypothyroidism, unspecified

  • E04|

    Other nontoxic goiter

  • E04.0|

    Nontoxic diffuse goiter

  • E04.1|

    Nontoxic single thyroid nodule

  • E04.2|

    Nontoxic multinodular goiter

  • E04.8|

    Other specified nontoxic goiter

  • E04.9|

    Nontoxic goiter, unspecified

  • E05|

    Thyrotoxicosis [hyperthyroidism]

  • E05.0|

    Thyrotoxicosis with diffuse goiter

  • E05.00|

    Thyrotoxicosis with diffuse goiter without thyrotoxic crisis or storm

  • E05.01|

    Thyrotoxicosis with diffuse goiter with thyrotoxic crisis or storm

  • E05.1|

    Thyrotoxicosis with toxic single thyroid nodule

  • E05.10|

    Thyrotoxicosis with toxic single thyroid nodule without thyrotoxic crisis or storm

  • E05.11|

    Thyrotoxicosis with toxic single thyroid nodule with thyrotoxic crisis or storm

  • E05.2|

    Thyrotoxicosis with toxic multinodular goiter

  • E05.20|

    Thyrotoxicosis with toxic multinodular goiter without thyrotoxic crisis or storm

  • E05.21|

    Thyrotoxicosis with toxic multinodular goiter with thyrotoxic crisis or storm

  • E05.3|

    Thyrotoxicosis from ectopic thyroid tissue

  • E05.30|

    Thyrotoxicosis from ectopic thyroid tissue without thyrotoxic crisis or storm

  • E05.31|

    Thyrotoxicosis from ectopic thyroid tissue with thyrotoxic crisis or storm

  • E05.4|

    Thyrotoxicosis factitia

  • E05.40|

    Thyrotoxicosis factitia without thyrotoxic crisis or storm

  • E05.41|

    Thyrotoxicosis factitia with thyrotoxic crisis or storm

  • E05.8|

    Other thyrotoxicosis

  • E05.80|

    Other thyrotoxicosis without thyrotoxic crisis or storm

  • E05.81|

    Other thyrotoxicosis with thyrotoxic crisis or storm

  • E05.9|

    Thyrotoxicosis, unspecified

  • E05.90|

    Thyrotoxicosis, unspecified without thyrotoxic crisis or storm

  • E05.91|

    Thyrotoxicosis, unspecified with thyrotoxic crisis or storm

  • E06|

    Thyroiditis

  • E06.0|

    Acute thyroiditis

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