All ICD10 Codes
Chapter 4

E00–E89: Endocrine, Nutritional and Metabolic Diseases

Endocrine, Nutritional and Metabolic Diseases diagnostic classification updated for 2026.

Chapter Instructions

Excludes1(Not coded here. Use a different code.)
  • transitory endocrine and metabolic disorders specific to newborn (P70-P74)
All CodesBillable Only
Internal Codes
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  • E74.4—

    Disorders of pyruvate metabolism and gluconeogenesis

  • E74.810—

    Glucose transporter protein type 1 deficiency

  • E74.818—

    Other disorders of glucose transport

  • E74.819—

    Disorders of glucose transport, unspecified

  • E74.820—

    SLC13A5 Citrate Transporter Disorder

  • E74.829—

    Other disorders of citrate metabolism

  • E74.89—

    Other specified disorders of carbohydrate metabolism

  • E74.9—

    Disorder of carbohydrate metabolism, unspecified

  • E75.00—

    GM2 gangliosidosis, unspecified

  • E75.01—

    Sandhoff disease

  • E75.02—

    Tay-Sachs disease

  • E75.09—

    Other GM2 gangliosidosis

  • E75.10—

    Unspecified gangliosidosis

  • E75.11—

    Mucolipidosis IV

  • E75.19—

    Other gangliosidosis

  • E75.21—

    Fabry (-Anderson) disease

  • E75.22—

    Gaucher disease

  • E75.23—

    Krabbe disease

  • E75.240—

    Niemann-Pick disease type A

  • E75.241—

    Niemann-Pick disease type B

  • E75.242—

    Niemann-Pick disease type C

  • E75.243—

    Niemann-Pick disease type D

  • E75.244—

    Niemann-Pick disease type A/B

  • E75.248—

    Other Niemann-Pick disease

  • E75.249—

    Niemann-Pick disease, unspecified

  • E75.25—

    Metachromatic leukodystrophy

  • E75.26—

    Sulfatase deficiency

  • E75.27—

    Pelizaeus-Merzbacher disease

  • E75.28—

    Canavan disease

  • E75.29—

    Other sphingolipidosis

  • E75.3—

    Sphingolipidosis, unspecified

  • E75.4—

    Neuronal ceroid lipofuscinosis

  • E75.5—

    Other lipid storage disorders

  • E75.6—

    Lipid storage disorder, unspecified

  • E76.01—

    Hurler's syndrome

  • E76.02—

    Hurler-Scheie syndrome

  • E76.03—

    Scheie's syndrome

  • E76.1—

    Mucopolysaccharidosis, type II

  • E76.210—

    Morquio A mucopolysaccharidoses

  • E76.211—

    Morquio B mucopolysaccharidoses

  • E76.219—

    Morquio mucopolysaccharidoses, unspecified

  • E76.22—

    Sanfilippo mucopolysaccharidoses

  • E76.29—

    Other mucopolysaccharidoses

  • E76.3—

    Mucopolysaccharidosis, unspecified

  • E76.8—

    Other disorders of glucosaminoglycan metabolism

  • E76.9—

    Glucosaminoglycan metabolism disorder, unspecified

  • E77.0—

    Defects in post-translational modification of lysosomal enzymes

  • E77.1—

    Defects in glycoprotein degradation

  • E77.8—

    Other disorders of glycoprotein metabolism

  • E77.9—

    Disorder of glycoprotein metabolism, unspecified

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