E00–E89: Endocrine, Nutritional and Metabolic Diseases
Chapter 4 of ICD-10-CM 2027, 1,270 codes in 10 blocks.
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Chapter instructions
Excludes1: not coded here, use a different code
- transitory endocrine and metabolic disorders specific to newborn (P70-P74)
Codes in this chapter
All codesBillable only973 results
- E78.81Lipoid dermatoarthritis
- E78.89Other lipoprotein metabolism disorders
- E78.9Disorder of lipoprotein metabolism, unspecified
- E79.0Hyperuricemia without signs of inflammatory arthritis and tophaceous disease
- E79.1Lesch-Nyhan syndrome
- E79.2Myoadenylate deaminase deficiency
- E79.81Aicardi-Goutieres syndrome
- E79.82Hereditary xanthinuria
- E79.89Other specified disorders of purine and pyrimidine metabolism
- E79.9Disorder of purine and pyrimidine metabolism, unspecified
- E80.0Hereditary erythropoietic porphyria
- E80.1Porphyria cutanea tarda
- E80.20Unspecified porphyria
- E80.21Acute intermittent (hepatic) porphyria
- E80.29Other porphyria
- E80.3Defects of catalase and peroxidase
- E80.4Gilbert syndrome
- E80.5Crigler-Najjar syndrome
- E80.6Other disorders of bilirubin metabolism
- E80.7Disorder of bilirubin metabolism, unspecified
- E83.00Disorder of copper metabolism, unspecified
- E83.01Wilson's disease
- E83.09Other disorders of copper metabolism
- E83.10Disorder of iron metabolism, unspecified
- E83.110Hereditary hemochromatosis
- E83.111Hemochromatosis due to repeated red blood cell transfusions
- E83.118Other hemochromatosis
- E83.119Hemochromatosis, unspecified
- E83.19Other disorders of iron metabolism
- E83.2Disorders of zinc metabolism
- E83.30Disorder of phosphorus metabolism, unspecified
- E83.31Familial hypophosphatemia
- E83.32Hereditary vitamin D-dependent rickets (type 1) (type 2)
- E83.39Other disorders of phosphorus metabolism
- E83.40Disorders of magnesium metabolism, unspecified
- E83.41Hypermagnesemia
- E83.42Hypomagnesemia
- E83.49Other disorders of magnesium metabolism
- E83.50Unspecified disorder of calcium metabolism
- E83.51Hypocalcemia
- E83.52Hypercalcemia
- E83.59Other disorders of calcium metabolism
- E83.81Hungry bone syndrome
- E83.820Generalized arterial calcification of infancy with unspecified genetic causality
- E83.821ENPP1 deficiency causing generalized arterial calcification of infancy
- E83.822ENPP1 deficiency causing autosomal recessive hypophosphatemic rickets type 2
- E83.823ABCC6 deficiency causing generalized arterial calcification of infancy
- E83.824ABCC6 deficiency causing pseudoxanthoma elasticum
- E83.825CD73 deficiency causing arterial calcification
- E83.89Other disorders of mineral metabolism
