E00–E89: Endocrine, Nutritional and Metabolic Diseases
Chapter 4 of ICD-10-CM 2027, 1,270 codes in 10 blocks.
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Chapter instructions
Excludes1: not coded here, use a different code
- transitory endocrine and metabolic disorders specific to newborn (P70-P74)
Codes in this chapter
All codesBillable only973 results
- E72.4Disorders of ornithine metabolism
- E72.50Disorder of glycine metabolism, unspecified
- E72.51Non-ketotic hyperglycinemia
- E72.52Trimethylaminuria
- E72.530Primary hyperoxaluria, type 1
- E72.538Other specified primary hyperoxaluria
- E72.539Primary hyperoxaluria, unspecified
- E72.540Dietary hyperoxaluria
- E72.541Enteric hyperoxaluria
- E72.548Other secondary hyperoxaluria
- E72.549Secondary hyperoxaluria, unspecified
- E72.59Other disorders of glycine metabolism
- E72.81Disorders of gamma aminobutyric acid metabolism
- E72.89Other specified disorders of amino-acid metabolism
- E72.9Disorder of amino-acid metabolism, unspecified
- E73.0Congenital lactase deficiency
- E73.1Secondary lactase deficiency
- E73.8Other lactose intolerance
- E73.9Lactose intolerance, unspecified
- E74.00Glycogen storage disease, unspecified
- E74.01von Gierke disease
- E74.02Pompe disease
- E74.03Cori disease
- E74.04McArdle disease
- E74.05Lysosome-associated membrane protein 2 [LAMP2] deficiency
- E74.09Other glycogen storage disease
- E74.10Disorder of fructose metabolism, unspecified
- E74.11Essential fructosuria
- E74.12Hereditary fructose intolerance
- E74.19Other disorders of fructose metabolism
- E74.20Disorders of galactose metabolism, unspecified
- E74.21Galactosemia
- E74.29Other disorders of galactose metabolism
- E74.31Sucrase-isomaltase deficiency
- E74.39Other disorders of intestinal carbohydrate absorption
- E74.4Disorders of pyruvate metabolism and gluconeogenesis
- E74.810Glucose transporter protein type 1 deficiency
- E74.818Other disorders of glucose transport
- E74.819Disorders of glucose transport, unspecified
- E74.820SLC13A5 Citrate Transporter Disorder
- E74.829Other disorders of citrate metabolism
- E74.89Other specified disorders of carbohydrate metabolism
- E74.9Disorder of carbohydrate metabolism, unspecified
- E75.00GM2 gangliosidosis, unspecified
- E75.01Sandhoff disease
- E75.02Tay-Sachs disease
- E75.09Other GM2 gangliosidosis
- E75.10Unspecified gangliosidosis
- E75.11Mucolipidosis IV
- E75.19Other gangliosidosis
