All ICD10 Codes
Chapter 4

E00–E89: Endocrine, Nutritional and Metabolic Diseases

Endocrine, Nutritional and Metabolic Diseases diagnostic classification updated for 2026.

Chapter Instructions

Excludes1(Not coded here. Use a different code.)
  • transitory endocrine and metabolic disorders specific to newborn (P70-P74)
All CodesBillable Only
Internal Codes
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  • E70.331—

    Hermansky-Pudlak syndrome

  • E70.338—

    Other albinism with hematologic abnormality

  • E70.339—

    Albinism with hematologic abnormality, unspecified

  • E70.39—

    Other specified albinism

  • E70.40—

    Disorders of histidine metabolism, unspecified

  • E70.41—

    Histidinemia

  • E70.49—

    Other disorders of histidine metabolism

  • E70.5—

    Disorders of tryptophan metabolism

  • E70.81—

    Aromatic L-amino acid decarboxylase deficiency

  • E70.89—

    Other disorders of aromatic amino-acid metabolism

  • E70.9—

    Disorder of aromatic amino-acid metabolism, unspecified

  • E71.0—

    Maple-syrup-urine disease

  • E71.110—

    Isovaleric acidemia

  • E71.111—

    3-methylglutaconic aciduria

  • E71.118—

    Other branched-chain organic acidurias

  • E71.120—

    Methylmalonic acidemia

  • E71.121—

    Propionic acidemia

  • E71.128—

    Other disorders of propionate metabolism

  • E71.19—

    Other disorders of branched-chain amino-acid metabolism

  • E71.2—

    Disorder of branched-chain amino-acid metabolism, unspecified

  • E71.30—

    Disorder of fatty-acid metabolism, unspecified

  • E71.310—

    Long chain/very long chain acyl CoA dehydrogenase deficiency

  • E71.311—

    Medium chain acyl CoA dehydrogenase deficiency

  • E71.312—

    Short chain acyl CoA dehydrogenase deficiency

  • E71.313—

    Glutaric aciduria type II

  • E71.314—

    Muscle carnitine palmitoyltransferase deficiency

  • E71.318—

    Other disorders of fatty-acid oxidation

  • E71.32—

    Disorders of ketone metabolism

  • E71.39—

    Other disorders of fatty-acid metabolism

  • E71.40—

    Disorder of carnitine metabolism, unspecified

  • E71.41—

    Primary carnitine deficiency

  • E71.42—

    Carnitine deficiency due to inborn errors of metabolism

  • E71.43—

    Iatrogenic carnitine deficiency

  • E71.440—

    Ruvalcaba-Myhre-Smith syndrome

  • E71.448—

    Other secondary carnitine deficiency

  • E71.50—

    Peroxisomal disorder, unspecified

  • E71.510—

    Zellweger syndrome

  • E71.511—

    Neonatal adrenoleukodystrophy

  • E71.518—

    Other disorders of peroxisome biogenesis

  • E71.520—

    Childhood cerebral X-linked adrenoleukodystrophy

  • E71.521—

    Adolescent X-linked adrenoleukodystrophy

  • E71.522—

    Adrenomyeloneuropathy

  • E71.528—

    Other X-linked adrenoleukodystrophy

  • E71.529—

    X-linked adrenoleukodystrophy, unspecified type

  • E71.53—

    Other group 2 peroxisomal disorders

  • E71.540—

    Rhizomelic chondrodysplasia punctata

  • E71.541—

    Zellweger-like syndrome

  • E71.542—

    Other group 3 peroxisomal disorders

  • E71.548—

    Other peroxisomal disorders

  • E72.00—

    Disorders of amino-acid transport, unspecified

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