All ICD10 Codes

E88.01

Billable
ChapterE00–E89
Ranksubcategory
Official Description

Alpha-1-antitrypsin deficiency

Metadata & Insights
  • •Billable/specific code (valid for reimbursement).
  • •Chapter 4: Endocrine, Nutritional and Metabolic Diseases (E00-E89).

Instructional Notes

Includes
  • AAT deficiency
General instructions are available for the parent sections:
View CH4 NotesView E70-E88 NotesView E88 NotesView E88.0 Notes

Clinical Hierarchy

BillableHas subcodes
CH4Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88Metabolic disorders (E70-E88)
E88Other and unspecified metabolic disorders
E88.0Disorders of plasma-protein metabolism, not elsewhere classified
E88.01Alpha-1-antitrypsin deficiencyBillable

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to E88.01:

subcategoryE88.0
Disorders of plasma-protein metabolism, not elsewhere classified
View context instructions
categoryE88
Other and unspecified metabolic disorders
View context instructions
blockE70-E88
Metabolic disorders (E70-E88)
View context instructions
chapterCH4
Endocrine, nutritional and metabolic diseases (E00-E89)
View context instructions

MS-DRG Classification

2026 v43.1

This code is grouped within the following Diagnosis Related Group(s) for clinical reimbursement:

DRG 642
Inborn and Other Disorders of Metabolism

Cross Reference

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