G11.11

Billable
ChapterG00–G99
Ranksubcategory
Official Description

Friedreich ataxia

Metadata & Insights
  • •2026 ICD-10-CM Edition - Effective October 1, 2025.
  • •Billable/specific code (valid for reimbursement).
  • •Chapter 6: Diseases of the Nervous System (G00-G99).

Instructional Notes

Includes
  • Autosomal recessive Friedreich ataxia
  • Friedreich ataxia with retained reflexes
General instructions are available for the parent sections:
View CH6 NotesView G11 Notes

Clinical Hierarchy

CH6Diseases of the nervous system (G00-G99)
G10-G14Systemic atrophies primarily affecting the central nervous system (G10-G14)
G11Hereditary ataxia
G11.1Early-onset cerebellar ataxia
G11.11Friedreich ataxia

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to G11.11:

categoryG11
Hereditary ataxia
View context instructions
chapterCH6
Diseases of the nervous system (G00-G99)
View context instructions

Alphabetic Index Mentions

These are Diagnosis Index lookup paths that route to G11.11. Use them as entry terms for search, then confirm final coding instructions in the Tabular List and notes above.

13 raw paths
Ataxia, ataxy, ataxic4 unique routes
autosomal recessive Friedreich→G11.11
Friedreich's (heredofamilial) (cerebellar) (spinal) (with retained reflexes)→G11.11
hereditary
spinal (Friedreich's)→G11.11
spinal
hereditary (Friedreich's)→G11.11
Cardiomyopathy (familial) (idiopathic)1 unique routes
due to
Friedreich's ataxia→G11.11
Disease, diseased1 unique routes
Friedreich's
combined systemic or ataxia→G11.11
Friedreich's3 unique routes
ataxia→G11.11
combined systemic disease→G11.11
sclerosis (cerebellum) (spinal cord)→G11.11
Myocardiopathy (congestive) (constrictive) (familial) (hypertrophic nonobstructive) (idiopathic) (infiltrative) (obstructive) (primary) (restrictive) (sporadic)1 unique routes
in (due to)
Friedreich's ataxia→G11.11
Sclerosis, sclerotic3 unique routes
Friedreich's (spinal cord)→G11.11
hereditary
spinal (Friedreich's ataxia)→G11.11
spinal (cord) (progressive)
hereditary (Friedreich's) (mixed form)→G11.11

MS-DRG Classification

2026 v43.1

This code is grouped within the following Diagnosis Related Group(s) for clinical reimbursement:

DRG 058
Multiple Sclerosis and Cerebellar Ataxia with MCC
DRG 059
Multiple Sclerosis and Cerebellar Ataxia with CC
DRG 060
Multiple Sclerosis and Cerebellar Ataxia without CC/MCC

Cross Reference

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