G11.1

Non-Billable
ChapterG00–G99
Ranksubcategory
Official Description

Early-onset cerebellar ataxia

Metadata & Insights
  • •2026 ICD-10-CM Edition - Effective October 1, 2025.
  • •Non-billable category (requires more specific sub-code).
  • •Chapter 6: Diseases of the Nervous System (G00-G99).
General instructions are available for the parent sections:
View CH6 NotesView G11 Notes

Clinical Hierarchy

CH6Diseases of the nervous system (G00-G99)
G10-G14Systemic atrophies primarily affecting the central nervous system (G10-G14)
G11Hereditary ataxia
G11.1Early-onset cerebellar ataxia
G11.10Early-onset cerebellar ataxia, unspecified
G11.11Friedreich ataxia
G11.19Other early-onset cerebellar ataxia

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to G11.1:

categoryG11
Hereditary ataxia
View context instructions
chapterCH6
Diseases of the nervous system (G00-G99)
View context instructions

Alphabetic Index Mentions

These are Diagnosis Index lookup paths that route to G11.1. Use them as entry terms for search, then confirm final coding instructions in the Tabular List and notes above.

24 raw paths
Ataxia, ataxy, ataxic10 unique routes
autosomal recessive Friedreich→G11.1
cerebellar (hereditary)(4 variants)
early-onset→G11.1
with(3 variants)
essential tremor→G11.1
myoclonus [Hunt's ataxia]→G11.1
retained tendon reflexes→G11.1
Friedreich's (heredofamilial) (cerebellar) (spinal) (with retained reflexes)→G11.1
hereditary
spinal (Friedreich's)→G11.1
Hunt's→G11.1
spinal
hereditary (Friedreich's)→G11.1
spinocerebellar, X-linked recessive→G11.1
Cardiomyopathy (familial) (idiopathic)1 unique routes
due to
Friedreich's ataxia→G11.1
Disease, diseased2 unique routes
Friedreich's
combined systemic or ataxia→G11.1
Hunt's (herpetic geniculate ganglionitis) (neuralgia)
dyssynergia cerebellaris myoclonica→G11.1
Dyssynergia1 unique routes
cerebellaris myoclonica (Hunt's ataxia)→G11.1
Friedreich's3 unique routes
ataxia→G11.1
combined systemic disease→G11.1
sclerosis (cerebellum) (spinal cord)→G11.1
Hunt's1 unique routes
disease or syndrome (herpetic geniculate ganglionitis)
dyssynergia cerebellaris myoclonica→G11.1
Myocardiopathy (congestive) (constrictive) (familial) (hypertrophic nonobstructive) (idiopathic) (infiltrative) (obstructive) (primary) (restrictive) (sporadic)1 unique routes
in (due to)
Friedreich's ataxia→G11.1
Ramsay-Hunt disease or syndrome1 unique routes
meaning dyssynergia cerebellaris myoclonica→G11.1
Sclerosis, sclerotic3 unique routes
Friedreich's (spinal cord)→G11.1
hereditary
spinal (Friedreich's ataxia)→G11.1
spinal (cord) (progressive)
hereditary (Friedreich's) (mixed form)→G11.1
Syndrome1 unique routes
Hunt's (herpetic geniculate ganglionitis) (neuralgia)
dyssynergia cerebellaris myoclonica→G11.1

MS-DRG Classification

2026

No direct MS-DRG triggers identified.

Cross Reference

Find Procedures (ICD-10-PCS)

Find surgical and procedural codes related to Early-onset cerebellar ataxia.

Search PCS Codes