E75.27

Billable

ChapterE00–E89

Ranksubcategory

Official Description

Pelizaeus-Merzbacher disease

Metadata & Insights

•2026 ICD-10-CM Edition - Effective October 1, 2025.
•Billable/specific code (valid for reimbursement).
•Chapter 4: Endocrine, Nutritional and Metabolic Diseases (E00-E89).

General instructions are available for the parent sections:

View CH4 Notes View E70-E88 Notes View E75 Notes View E75.2 Notes

Clinical Hierarchy

CH4Endocrine, nutritional and metabolic diseases (E00-E89)

E70-E88Metabolic disorders (E70-E88)

E75Disorders of sphingolipid metabolism and other lipid storage disorders

E75.2Other sphingolipidosis

E75.27Pelizaeus-Merzbacher disease

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to E75.27:

subcategoryE75.2

Other sphingolipidosis

View context instructions

categoryE75

Disorders of sphingolipid metabolism and other lipid storage disorders

View context instructions

blockE70-E88

Metabolic disorders (E70-E88)

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chapterCH4

Endocrine, nutritional and metabolic diseases (E00-E89)

View context instructions

Alphabetic Index Mentions

These are Diagnosis Index lookup paths that route to E75.27. Use them as entry terms for search, then confirm final coding instructions in the Tabular List and notes above.

3 raw paths

Aplasia1 unique routes

Pelizaeus-Merzbacher→E75.27

Merzbacher-Pelizaeus disease1 unique routes

Direct index entry→E75.27

Pelizaeus-Merzbacher disease1 unique routes

Direct index entry→E75.27

MS-DRG Classification

2026 v43.1

This code is grouped within the following Diagnosis Related Group(s) for clinical reimbursement:

DRG 056

Degenerative Nervous System Disorders with MCC

DRG 057

Degenerative Nervous System Disorders without MCC

Cross Reference

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