E72.11

Billable
ChapterE00–E89
Ranksubcategory
Official Description

Homocystinuria

Metadata & Insights
  • •2026 ICD-10-CM Edition - Effective October 1, 2025.
  • •Billable/specific code (valid for reimbursement).
  • •Chapter 4: Endocrine, Nutritional and Metabolic Diseases (E00-E89).

Instructional Notes

Includes
  • Cystathionine synthase deficiency
General instructions are available for the parent sections:
View CH4 NotesView E70-E88 NotesView E72 NotesView E72.1 Notes

Clinical Hierarchy

CH4Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88Metabolic disorders (E70-E88)
E72Other disorders of amino-acid metabolism
E72.1Disorders of sulfur-bearing amino-acid metabolism
E72.11Homocystinuria

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to E72.11:

subcategoryE72.1
Disorders of sulfur-bearing amino-acid metabolism
View context instructions
categoryE72
Other disorders of amino-acid metabolism
View context instructions
blockE70-E88
Metabolic disorders (E70-E88)
View context instructions
chapterCH4
Endocrine, nutritional and metabolic diseases (E00-E89)
View context instructions

Alphabetic Index Mentions

These are Diagnosis Index lookup paths that route to E72.11. Use them as entry terms for search, then confirm final coding instructions in the Tabular List and notes above.

5 raw paths
Cystathionine synthase deficiency1 unique routes
Direct index entry→E72.11
Disorder (of)2 unique routes
amino-acid
homocystinuria→E72.11
metabolism NOS
amino-acid
sulfur-bearing
homocystinuria→E72.11
Homocystinuria1 unique routes
Direct index entry→E72.11
Hyperhomocysteinemia1 unique routes
Direct index entry→E72.11

MS-DRG Classification

2026 v43.1

This code is grouped within the following Diagnosis Related Group(s) for clinical reimbursement:

DRG 642
Inborn and Other Disorders of Metabolism

Cross Reference

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