E70.321

Billable
ChapterE00–E89
Ranksubcategory
Official Description

Tyrosinase positive oculocutaneous albinism

Metadata & Insights
  • 2026 ICD-10-CM Edition - Effective October 1, 2025.
  • Billable/specific code (valid for reimbursement).
  • Chapter 4: Endocrine, Nutritional and Metabolic Diseases (E00-E89).

Instructional Notes

Includes
  • Albinism II
  • Oculocutaneous albinism ty-pos
General instructions are available for the parent sections:

Clinical Hierarchy

CH4Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88Metabolic disorders (E70-E88)
E70Disorders of aromatic amino-acid metabolism
E70.3Albinism
E70.32Oculocutaneous albinism
E70.321Tyrosinase positive oculocutaneous albinism

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to E70.321:

subcategoryE70.32
Oculocutaneous albinism
View context instructions
blockE70-E88
Metabolic disorders (E70-E88)
View context instructions
chapterCH4
Endocrine, nutritional and metabolic diseases (E00-E89)
View context instructions

Alphabetic Index Mentions

These are Diagnosis Index lookup paths that route to E70.321. Use them as entry terms for search, then confirm final coding instructions in the Tabular List and notes above.

2 raw paths

MS-DRG Classification

2026 v43.1

This code is grouped within the following Diagnosis Related Group(s) for clinical reimbursement:

Cross Reference

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