D61.01

Billable
ChapterD50–D89
Ranksubcategory
Official Description

Constitutional (pure) red blood cell aplasia

Metadata & Insights
  • •2026 ICD-10-CM Edition - Effective October 1, 2025.
  • •Billable/specific code (valid for reimbursement).
  • •Chapter 3: Diseases of the Blood and Blood-Forming Organs (D50-D89).

Instructional Notes

Includes
  • Blackfan-Diamond syndrome
  • Congenital (pure) red cell aplasia
  • Familial hypoplastic anemia
  • Primary (pure) red cell aplasia
  • Red cell (pure) aplasia of infants
Excludes1(Not coded here)
  • acquired red cell aplasia (D60.9)
General instructions are available for the parent sections:
View CH3 NotesView D61 Notes

Clinical Hierarchy

CH3Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
D60-D64Aplastic and other anemias and other bone marrow failure syndromes (D60-D64)
D61Other aplastic anemias and other bone marrow failure syndromes
D61.0Constitutional aplastic anemia
D61.01Constitutional (pure) red blood cell aplasia

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to D61.01:

categoryD61
Other aplastic anemias and other bone marrow failure syndromes
View context instructions
chapterCH3
Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
View context instructions

Alphabetic Index Mentions

These are Diagnosis Index lookup paths that route to D61.01. Use them as entry terms for search, then confirm final coding instructions in the Tabular List and notes above.

24 raw paths
Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound)6 unique routes
aplastic
red cell (pure)
congenital→D61.01
Diamond-Blackfan (congenital hypoplastic)→D61.01
hypoplasia, red blood cells
congenital or familial→D61.01
hypoplastic (idiopathic)
congenital or familial (of childhood)→D61.01
Joseph-Diamond-Blackfan (congenital hypoplastic)→D61.01
pure red cell
congenital→D61.01
Aplasia9 unique routes
bone marrow (myeloid)
congenital→D61.01
congenital pure red cell→D61.01
erythrocyte congenital→D61.01
red cell (with thymoma)(6 variants)
congenital→D61.01
constitutional→D61.01
hereditary→D61.01
of infants→D61.01
primary→D61.01
pure→D61.01
Blackfan-Diamond anemia or syndrome (congenital hypoplastic anemia)1 unique routes
Direct index entry→D61.01
Diamond-Blackfan anemia (congenital hypoplastic)1 unique routes
Direct index entry→D61.01
Erythroblastopenia1 unique routes
congenital→D61.01
Hypoplasia, hypoplastic1 unique routes
erythroid, congenital→D61.01
Joseph-Diamond-Blackfan anemia (congenital hypoplastic)1 unique routes
Direct index entry→D61.01
Kaznelson's syndrome (congenital hypoplastic anemia)1 unique routes
Direct index entry→D61.01
Syndrome3 unique routes
Blackfan-Diamond→D61.01
Diamond-Blackfan→D61.01
Joseph-Diamond-Blackfan→D61.01

MS-DRG Classification

2026 v43.1

This code is grouped within the following Diagnosis Related Group(s) for clinical reimbursement:

DRG 808
Major Hematological and Immunological Diagnoses Except Sickle Cell Crisis and Coagulation Disorders with MCC
DRG 809
Major Hematological and Immunological Diagnoses Except Sickle Cell Crisis and Coagulation Disorders with CC
DRG 810
Major Hematological and Immunological Diagnoses Except Sickle Cell Crisis and Coagulation Disorders without CC/MCC

Cross Reference

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