N01.1

Billable
ChapterN00–N99
Ranksubcategory
Official Description

Rapidly progressive nephritic syndrome with focal and segmental glomerular lesions

Metadata & Insights
  • •2026 ICD-10-CM Edition - Effective October 1, 2025.
  • •Billable/specific code (valid for reimbursement).
  • •Chapter 14: Diseases of the Genitourinary System (N00-N99).

Instructional Notes

Includes
  • Rapidly progressive nephritic syndrome with focal and segmental hyalinosis
  • Rapidly progressive nephritic syndrome with focal and segmental sclerosis
  • Rapidly progressive nephritic syndrome with focal glomerulonephritis
General instructions are available for the parent sections:
View CH14 NotesView N00-N08 NotesView N01 Notes

Clinical Hierarchy

CH14Diseases of the genitourinary system (N00-N99)
N00-N08Glomerular diseases (N00-N08)
N01Rapidly progressive nephritic syndrome
N01.1Rapidly progressive nephritic syndrome with focal and segmental glomerular lesions

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to N01.1:

categoryN01
Rapidly progressive nephritic syndrome
View context instructions
blockN00-N08
Glomerular diseases (N00-N08)
View context instructions
chapterCH14
Diseases of the genitourinary system (N00-N99)
View context instructions

Alphabetic Index Mentions

These are Diagnosis Index lookup paths that route to N01.1. Use them as entry terms for search, then confirm final coding instructions in the Tabular List and notes above.

1 raw paths
Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)1 unique routes
rapidly progressive
with
focal and segmental glomerular lesions→N01.1

MS-DRG Classification

2026 v43.1

This code is grouped within the following Diagnosis Related Group(s) for clinical reimbursement:

DRG 698
Other Kidney and Urinary Tract Diagnoses with MCC
DRG 699
Other Kidney and Urinary Tract Diagnoses with CC
DRG 700
Other Kidney and Urinary Tract Diagnoses without CC/MCC
DRG 791
Prematurity with Major Problems
DRG 793
Full Term Neonate with Major Problems

Cross Reference

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