N01

Non-Billable

ChapterN00–N99

Rankcategory

Official Description

Rapidly progressive nephritic syndrome

Metadata & Insights

•2026 ICD-10-CM Edition - Effective October 1, 2025.
•Non-billable category (requires more specific sub-code).
•Chapter 14: Diseases of the Genitourinary System (N00-N99).

CH14 Parent Instructions

Excludes2(Not included here)

certain conditions originating in the perinatal period (P04-P96)
certain infectious and parasitic diseases (A00-B99)
complications of pregnancy, childbirth and the puerperium (O00-O9A)
congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
endocrine, nutritional and metabolic diseases (E00-E88)
injury, poisoning and certain other consequences of external causes (S00-T88)
neoplasms (C00-D49)
symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)

N00-N08 Parent Instructions

Excludes1(Not coded here)

hypertensive chronic kidney disease (I12.-)

Code Also

any associated kidney failure (N17-N19).

Instructional Notes

Includes

rapidly progressive glomerular disease
rapidly progressive glomerulonephritis
rapidly progressive nephritis

Excludes1(Not coded here)

nephritic syndrome NOS (N05.-)

Clinical Hierarchy

CH14Diseases of the genitourinary system (N00-N99)

N00-N08Glomerular diseases (N00-N08)

N01Rapidly progressive nephritic syndrome

N01.0Rapidly progressive nephritic syndrome with minor glomerular abnormality

N01.1Rapidly progressive nephritic syndrome with focal and segmental glomerular lesions

N01.2Rapidly progressive nephritic syndrome with diffuse membranous glomerulonephritis

N01.3Rapidly progressive nephritic syndrome with diffuse mesangial proliferative glomerulonephritis

N01.4Rapidly progressive nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis

N01.5Rapidly progressive nephritic syndrome with diffuse mesangiocapillary glomerulonephritis

N01.6Rapidly progressive nephritic syndrome with dense deposit disease

N01.7Rapidly progressive nephritic syndrome with diffuse crescentic glomerulonephritis

N01.8Rapidly progressive nephritic syndrome with other morphologic changes

N01.9Rapidly progressive nephritic syndrome with unspecified morphologic changes

N01.ARapidly progressive nephritic syndrome with C3 glomerulonephritis

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to N01:

blockN00-N08

Glomerular diseases (N00-N08)

View context instructions

chapterCH14

Diseases of the genitourinary system (N00-N99)

View context instructions

Alphabetic Index Mentions

These are Diagnosis Index lookup paths that route to N01. Use them as entry terms for search, then confirm final coding instructions in the Tabular List and notes above.

22 raw paths

Disease, diseased3 unique routes

glomerular

rapidly progressive→N01

renal (functional) (pelvis)(2 variants)

rapidly progressive→N01

subacute→N01

Glomerulonephritis3 unique routes

poststreptococcal NEC

rapidly progressive→N01

subacute→N01