A81.09

Billable
ChapterA00–B99
Ranksubcategory
Official Description

Other Creutzfeldt-Jakob disease

Metadata & Insights
  • •2026 ICD-10-CM Edition - Effective October 1, 2025.
  • •Billable/specific code (valid for reimbursement).
  • •Chapter 1: Certain Infectious and Parasitic Diseases (A00-B99).

Instructional Notes

Includes
  • CJD
  • Familial Creutzfeldt-Jakob disease
  • Iatrogenic Creutzfeldt-Jakob disease
  • Sporadic Creutzfeldt-Jakob disease
  • Subacute spongiform encephalopathy (with dementia)
General instructions are available for the parent sections:
View CH1 NotesView A80-A89 NotesView A81 Notes

Clinical Hierarchy

CH1Certain infectious and parasitic diseases (A00-B99)
A80-A89Viral and prion infections of the central nervous system (A80-A89)
A81Atypical virus infections of central nervous system
A81.0Creutzfeldt-Jakob disease
A81.09Other Creutzfeldt-Jakob disease

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to A81.09:

categoryA81
Atypical virus infections of central nervous system
View context instructions
blockA80-A89
Viral and prion infections of the central nervous system (A80-A89)
View context instructions
chapterCH1
Certain infectious and parasitic diseases (A00-B99)
View context instructions

Alphabetic Index Mentions

These are Diagnosis Index lookup paths that route to A81.09. Use them as entry terms for search, then confirm final coding instructions in the Tabular List and notes above.

5 raw paths
Creutzfeldt-Jakob disease or syndrome (with dementia)4 unique routes
familial→A81.09
iatrogenic→A81.09
specified NEC→A81.09
sporadic→A81.09
Encephalopathy (acute)1 unique routes
spongiform, subacute (viral)→A81.09

MS-DRG Classification

2026 v43.1

This code is grouped within the following Diagnosis Related Group(s) for clinical reimbursement:

DRG 056
Degenerative Nervous System Disorders with MCC
DRG 057
Degenerative Nervous System Disorders without MCC

Cross Reference

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