A81.0
Non-Billable
ChapterA00–B99
Ranksubcategory
Official Description
Creutzfeldt-Jakob disease
Metadata & Insights
- •2026 ICD-10-CM Edition - Effective October 1, 2025.
- •Non-billable category (requires more specific sub-code).
- •Chapter 1: Certain Infectious and Parasitic Diseases (A00-B99).
General instructions are available for the parent sections:
Clinical Hierarchy
CH1Certain infectious and parasitic diseases (A00-B99)
A80-A89Viral and prion infections of the central nervous system (A80-A89)
A81Atypical virus infections of central nervous system
A81.0Creutzfeldt-Jakob disease
A81.00Creutzfeldt-Jakob disease, unspecified
A81.01Variant Creutzfeldt-Jakob disease
A81.09Other Creutzfeldt-Jakob disease
Applicable Ancestor Context
The following parent sections contain instructions or notes that apply to A81.0:
blockA80-A89
Viral and prion infections of the central nervous system (A80-A89)
View context instructionsAlphabetic Index Mentions
These are Diagnosis Index lookup paths that route to A81.0. Use them as entry terms for search, then confirm final coding instructions in the Tabular List and notes above.
8 raw paths
Creutzfeldt-Jakob disease or syndrome (with dementia)6 unique routes
Encephalopathy (acute)1 unique routes
MS-DRG Classification
No direct MS-DRG triggers identified.
Cross Reference
Find Procedures (ICD-10-PCS)
Find surgical and procedural codes related to Creutzfeldt-Jakob disease.
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