All ICD10 Codes
Chapter 17

Q00–Q99: Congenital Malformations, Deformations and Chromosomal Abnormalities

Congenital Malformations, Deformations and Chromosomal Abnormalities diagnostic classification updated for 2026.

Chapter Instructions

Excludes2(Not included here. Code separately if applicable.)
  • inborn errors of metabolism (E70-E88)
All CodesBillable Only
Internal Codes
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  • Q44.0—

    Agenesis, aplasia and hypoplasia of gallbladder

  • Q44.1—

    Other congenital malformations of gallbladder

  • Q44.2—

    Atresia of bile ducts

  • Q44.3—

    Congenital stenosis and stricture of bile ducts

  • Q44.4—

    Choledochal cyst

  • Q44.5—

    Other congenital malformations of bile ducts

  • Q44.6—

    Cystic disease of liver

  • Q44.7—

    Other congenital malformations of liver

  • Q44.70—

    Other congenital malformation of liver, unspecified

  • Q44.71—

    Alagille syndrome

  • Q44.79—

    Other congenital malformations of liver

  • Q45—

    Other congenital malformations of digestive system

  • Q45.0—

    Agenesis, aplasia and hypoplasia of pancreas

  • Q45.1—

    Annular pancreas

  • Q45.2—

    Congenital pancreatic cyst

  • Q45.3—

    Other congenital malformations of pancreas and pancreatic duct

  • Q45.8—

    Other specified congenital malformations of digestive system

  • Q45.9—

    Congenital malformation of digestive system, unspecified

  • Q50—

    Congenital malformations of ovaries, fallopian tubes and broad ligaments

  • Q50.0—

    Congenital absence of ovary

  • Q50.01—

    Congenital absence of ovary, unilateral

  • Q50.02—

    Congenital absence of ovary, bilateral

  • Q50.1—

    Developmental ovarian cyst

  • Q50.2—

    Congenital torsion of ovary

  • Q50.3—

    Other congenital malformations of ovary

  • Q50.31—

    Accessory ovary

  • Q50.32—

    Ovarian streak

  • Q50.39—

    Other congenital malformation of ovary

  • Q50.4—

    Embryonic cyst of fallopian tube

  • Q50.5—

    Embryonic cyst of broad ligament

  • Q50.6—

    Other congenital malformations of fallopian tube and broad ligament

  • Q51—

    Congenital malformations of uterus and cervix

  • Q51.0—

    Agenesis and aplasia of uterus

  • Q51.1—

    Doubling of uterus with doubling of cervix and vagina

  • Q51.10—

    Doubling of uterus with doubling of cervix and vagina without obstruction

  • Q51.11—

    Doubling of uterus with doubling of cervix and vagina with obstruction

  • Q51.2—

    Other doubling of uterus

  • Q51.21—

    Complete doubling of uterus

  • Q51.22—

    Partial doubling of uterus

  • Q51.28—

    Other and unspecified doubling of uterus

  • Q51.3—

    Bicornate uterus

  • Q51.4—

    Unicornate uterus

  • Q51.5—

    Agenesis and aplasia of cervix

  • Q51.6—

    Embryonic cyst of cervix

  • Q51.7—

    Congenital fistulae between uterus and digestive and urinary tracts

  • Q51.8—

    Other congenital malformations of uterus and cervix

  • Q51.81—

    Other congenital malformations of uterus

  • Q51.810—

    Arcuate uterus

  • Q51.811—

    Hypoplasia of uterus

  • Q51.818—

    Other congenital malformations of uterus

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