Chapter 17

Q00–Q99: Congenital Malformations, Deformations and Chromosomal Abnormalities

Congenital Malformations, Deformations and Chromosomal Abnormalities diagnostic classification updated for 2026.

Chapter Instructions

Excludes2(Not included here. Code separately if applicable.)
  • inborn errors of metabolism (E70-E88)
Internal Codes
  • Q64.70

    Unspecified congenital malformation of bladder and urethra

  • Q64.71

    Congenital prolapse of urethra

  • Q64.72

    Congenital prolapse of urinary meatus

  • Q64.73

    Congenital urethrorectal fistula

  • Q64.74

    Double urethra

  • Q64.75

    Double urinary meatus

  • Q64.79

    Other congenital malformations of bladder and urethra

  • Q64.8

    Other specified congenital malformations of urinary system

  • Q64.9

    Congenital malformation of urinary system, unspecified

  • Q65

    Congenital deformities of hip

  • Q65.0

    Congenital dislocation of hip, unilateral

  • Q65.00

    Congenital dislocation of unspecified hip, unilateral

  • Q65.01

    Congenital dislocation of right hip, unilateral

  • Q65.02

    Congenital dislocation of left hip, unilateral

  • Q65.1

    Congenital dislocation of hip, bilateral

  • Q65.2

    Congenital dislocation of hip, unspecified

  • Q65.3

    Congenital partial dislocation of hip, unilateral

  • Q65.30

    Congenital partial dislocation of unspecified hip, unilateral

  • Q65.31

    Congenital partial dislocation of right hip, unilateral

  • Q65.32

    Congenital partial dislocation of left hip, unilateral

  • Q65.4

    Congenital partial dislocation of hip, bilateral

  • Q65.5

    Congenital partial dislocation of hip, unspecified

  • Q65.6

    Congenital unstable hip

  • Q65.8

    Other congenital deformities of hip

  • Q65.81

    Congenital coxa valga

  • Q65.82

    Congenital coxa vara

  • Q65.89

    Other specified congenital deformities of hip

  • Q65.9

    Congenital deformity of hip, unspecified

  • Q66

    Congenital deformities of feet

  • Q66.0

    Congenital talipes equinovarus

  • Q66.00

    Congenital talipes equinovarus, unspecified foot

  • Q66.01

    Congenital talipes equinovarus, right foot

  • Q66.02

    Congenital talipes equinovarus, left foot

  • Q66.1

    Congenital talipes calcaneovarus

  • Q66.10

    Congenital talipes calcaneovarus, unspecified foot

  • Q66.11

    Congenital talipes calcaneovarus, right foot

  • Q66.12

    Congenital talipes calcaneovarus, left foot

  • Q66.2

    Congenital metatarsus (primus) varus

  • Q66.21

    Congenital metatarsus primus varus

  • Q66.211

    Congenital metatarsus primus varus, right foot

  • Q66.212

    Congenital metatarsus primus varus, left foot

  • Q66.219

    Congenital metatarsus primus varus, unspecified foot

  • Q66.22

    Congenital metatarsus adductus

  • Q66.221

    Congenital metatarsus adductus, right foot

  • Q66.222

    Congenital metatarsus adductus, left foot

  • Q66.229

    Congenital metatarsus adductus, unspecified foot

  • Q66.3

    Other congenital varus deformities of feet

  • Q66.30

    Other congenital varus deformities of feet, unspecified foot

  • Q66.31

    Other congenital varus deformities of feet, right foot

  • Q66.32

    Other congenital varus deformities of feet, left foot

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