Chapter 17

Q00–Q99: Congenital Malformations, Deformations and Chromosomal Abnormalities

Congenital Malformations, Deformations and Chromosomal Abnormalities diagnostic classification updated for 2026.

Chapter Instructions

Excludes2(Not included here. Code separately if applicable.)
  • inborn errors of metabolism (E70-E88)
Internal Codes
  • Q64.70|

    Unspecified congenital malformation of bladder and urethra

  • Q64.71|

    Congenital prolapse of urethra

  • Q64.72|

    Congenital prolapse of urinary meatus

  • Q64.73|

    Congenital urethrorectal fistula

  • Q64.74|

    Double urethra

  • Q64.75|

    Double urinary meatus

  • Q64.79|

    Other congenital malformations of bladder and urethra

  • Q64.8|

    Other specified congenital malformations of urinary system

  • Q64.9|

    Congenital malformation of urinary system, unspecified

  • Q65|

    Congenital deformities of hip

  • Q65.0|

    Congenital dislocation of hip, unilateral

  • Q65.00|

    Congenital dislocation of unspecified hip, unilateral

  • Q65.01|

    Congenital dislocation of right hip, unilateral

  • Q65.02|

    Congenital dislocation of left hip, unilateral

  • Q65.1|

    Congenital dislocation of hip, bilateral

  • Q65.2|

    Congenital dislocation of hip, unspecified

  • Q65.3|

    Congenital partial dislocation of hip, unilateral

  • Q65.30|

    Congenital partial dislocation of unspecified hip, unilateral

  • Q65.31|

    Congenital partial dislocation of right hip, unilateral

  • Q65.32|

    Congenital partial dislocation of left hip, unilateral

  • Q65.4|

    Congenital partial dislocation of hip, bilateral

  • Q65.5|

    Congenital partial dislocation of hip, unspecified

  • Q65.6|

    Congenital unstable hip

  • Q65.8|

    Other congenital deformities of hip

  • Q65.81|

    Congenital coxa valga

  • Q65.82|

    Congenital coxa vara

  • Q65.89|

    Other specified congenital deformities of hip

  • Q65.9|

    Congenital deformity of hip, unspecified

  • Q66|

    Congenital deformities of feet

  • Q66.0|

    Congenital talipes equinovarus

  • Q66.00|

    Congenital talipes equinovarus, unspecified foot

  • Q66.01|

    Congenital talipes equinovarus, right foot

  • Q66.02|

    Congenital talipes equinovarus, left foot

  • Q66.1|

    Congenital talipes calcaneovarus

  • Q66.10|

    Congenital talipes calcaneovarus, unspecified foot

  • Q66.11|

    Congenital talipes calcaneovarus, right foot

  • Q66.12|

    Congenital talipes calcaneovarus, left foot

  • Q66.2|

    Congenital metatarsus (primus) varus

  • Q66.21|

    Congenital metatarsus primus varus

  • Q66.211|

    Congenital metatarsus primus varus, right foot

  • Q66.212|

    Congenital metatarsus primus varus, left foot

  • Q66.219|

    Congenital metatarsus primus varus, unspecified foot

  • Q66.22|

    Congenital metatarsus adductus

  • Q66.221|

    Congenital metatarsus adductus, right foot

  • Q66.222|

    Congenital metatarsus adductus, left foot

  • Q66.229|

    Congenital metatarsus adductus, unspecified foot

  • Q66.3|

    Other congenital varus deformities of feet

  • Q66.30|

    Other congenital varus deformities of feet, unspecified foot

  • Q66.31|

    Other congenital varus deformities of feet, right foot

  • Q66.32|

    Other congenital varus deformities of feet, left foot

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