All ICD10 Codes
Chapter 17

Q00–Q99: Congenital Malformations, Deformations and Chromosomal Abnormalities

Congenital Malformations, Deformations and Chromosomal Abnormalities diagnostic classification updated for 2026.

Chapter Instructions

Excludes2(Not included here. Code separately if applicable.)
  • inborn errors of metabolism (E70-E88)
All CodesBillable Only
Internal Codes
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  • Q18.3—

    Webbing of neck

  • Q18.4—

    Macrostomia

  • Q18.5—

    Microstomia

  • Q18.6—

    Macrocheilia

  • Q18.7—

    Microcheilia

  • Q18.8—

    Other specified congenital malformations of face and neck

  • Q18.9—

    Congenital malformation of face and neck, unspecified

  • Q20.0—

    Common arterial trunk

  • Q20.1—

    Double outlet right ventricle

  • Q20.2—

    Double outlet left ventricle

  • Q20.3—

    Discordant ventriculoarterial connection

  • Q20.4—

    Double inlet ventricle

  • Q20.5—

    Discordant atrioventricular connection

  • Q20.6—

    Isomerism of atrial appendages

  • Q20.8—

    Other congenital malformations of cardiac chambers and connections

  • Q20.9—

    Congenital malformation of cardiac chambers and connections, unspecified

  • Q21.0—

    Ventricular septal defect

  • Q21.10—

    Atrial septal defect, unspecified

  • Q21.11—

    Secundum atrial septal defect

  • Q21.12—

    Patent foramen ovale

  • Q21.13—

    Coronary sinus atrial septal defect

  • Q21.14—

    Superior sinus venosus atrial septal defect

  • Q21.15—

    Inferior sinus venosus atrial septal defect

  • Q21.16—

    Sinus venosus atrial septal defect, unspecified

  • Q21.19—

    Other specified atrial septal defect

  • Q21.20—

    Atrioventricular septal defect, unspecified as to partial or complete

  • Q21.21—

    Partial atrioventricular septal defect

  • Q21.22—

    Transitional atrioventricular septal defect

  • Q21.23—

    Complete atrioventricular septal defect

  • Q21.3—

    Tetralogy of Fallot

  • Q21.4—

    Aortopulmonary septal defect

  • Q21.8—

    Other congenital malformations of cardiac septa

  • Q21.9—

    Congenital malformation of cardiac septum, unspecified

  • Q22.0—

    Pulmonary valve atresia

  • Q22.1—

    Congenital pulmonary valve stenosis

  • Q22.2—

    Congenital pulmonary valve insufficiency

  • Q22.3—

    Other congenital malformations of pulmonary valve

  • Q22.4—

    Congenital tricuspid stenosis

  • Q22.5—

    Ebstein's anomaly

  • Q22.6—

    Hypoplastic right heart syndrome

  • Q22.8—

    Other congenital malformations of tricuspid valve

  • Q22.9—

    Congenital malformation of tricuspid valve, unspecified

  • Q23.0—

    Congenital stenosis of aortic valve

  • Q23.1—

    Congenital insufficiency of aortic valve

  • Q23.2—

    Congenital mitral stenosis

  • Q23.3—

    Congenital mitral insufficiency

  • Q23.4—

    Hypoplastic left heart syndrome

  • Q23.81—

    Bicuspid aortic valve

  • Q23.82—

    Congenital mitral valve cleft leaflet

  • Q23.88—

    Other congenital malformations of aortic and mitral valves

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