Congenital malformations of the urinary system (Q60-Q64)
chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities
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Official coding guidelines
From the ICD-10-CM Official Guidelines for Coding and Reporting, FY 2027 (CMS and NCHS). Links open the PDF at the right page.
Assign Q00-QA1 codes for documented congenital anomalies or genetic disorders at any age, coding non-inherent manifestations separately and sequencing Z38 first on the birth admission.
All codes under Q60-Q64
Q60-Q64 can't be used on a claim. Pick a billable code below; grey headings group them.
- Q60Renal agenesis and other reduction defects of kidney
- Q60.0Renal agenesis, unilateral
- Q60.1Renal agenesis, bilateral
- Q60.2Renal agenesis, unspecified
- Q60.3Renal hypoplasia, unilateral
- Q60.4Renal hypoplasia, bilateral
- Q60.5Renal hypoplasia, unspecified
- Q60.6Potter's syndrome
- Q61Cystic kidney disease
- Q61.0Congenital renal cyst
- Q61.00Congenital renal cyst, unspecified
- Q61.01Congenital single renal cyst
- Q61.02Congenital multiple renal cysts
- Q61.1Polycystic kidney, infantile type
- Q61.11Cystic dilatation of collecting ducts
- Q61.19Other polycystic kidney, infantile type
- Q61.2Polycystic kidney, adult type
- Q61.3Polycystic kidney, unspecified
- Q61.4Renal dysplasia
- Q61.5Medullary cystic kidney
- Q61.8Other cystic kidney diseases
- Q61.9Cystic kidney disease, unspecified
- Q62Congenital obstructive defects of renal pelvis and congenital malformations of ureter
- Q62.0Congenital hydronephrosis
- Q62.1Congenital occlusion of ureter
- Q62.10Congenital occlusion of ureter, unspecified
- Q62.11Congenital occlusion of ureteropelvic junction
- Q62.12Congenital occlusion of ureterovesical orifice
- Q62.2Congenital megaureter
- Q62.3Other obstructive defects of renal pelvis and ureter
- Q62.31Congenital ureterocele, orthotopic
- Q62.32Cecoureterocele
- Q62.39Other obstructive defects of renal pelvis and ureter
- Q62.4Agenesis of ureter
- Q62.5Duplication of ureter
- Q62.6Malposition of ureter
- Q62.60Malposition of ureter, unspecified
- Q62.61Deviation of ureter
- Q62.62Displacement of ureter
- Q62.63Anomalous implantation of ureter
- Q62.69Other malposition of ureter
- Q62.7Congenital vesico-uretero-renal reflux
- Q62.8Other congenital malformations of ureter
- Q63Other congenital malformations of kidney
- Q63.0Accessory kidney
- Q63.1Lobulated, fused and horseshoe kidney
- Q63.2Ectopic kidney
- Q63.3Hyperplastic and giant kidney
- Q63.8Other specified congenital malformations of kidney
- Q63.9Congenital malformation of kidney, unspecified
- Q64Other congenital malformations of urinary system
- Q64.0Epispadias
- Q64.1Exstrophy of urinary bladder
- Q64.10Exstrophy of urinary bladder, unspecified
- Q64.11Supravesical fissure of urinary bladder
- Q64.12Cloacal exstrophy of urinary bladder
- Q64.19Other exstrophy of urinary bladder
- Q64.2Congenital posterior urethral valves
- Q64.3Other atresia and stenosis of urethra and bladder neck
- Q64.31Congenital bladder neck obstruction
- Q64.32Congenital stricture of urethra
- Q64.33Congenital stricture of urinary meatus
- Q64.39Other atresia and stenosis of urethra and bladder neck
- Q64.4Malformation of urachus
- Q64.5Congenital absence of bladder and urethra
- Q64.6Congenital diverticulum of bladder
- Q64.7Other and unspecified congenital malformations of bladder and urethra
- Q64.70Unspecified congenital malformation of bladder and urethra
- Q64.71Congenital prolapse of urethra
- Q64.72Congenital prolapse of urinary meatus
- Q64.73Congenital urethrorectal fistula
- Q64.74Double urethra
- Q64.75Double urinary meatus
- Q64.79Other congenital malformations of bladder and urethra
- Q64.8Other specified congenital malformations of urinary system
- Q64.9Congenital malformation of urinary system, unspecified
Q60-Q64 MS-DRGs
This code does not group to an MS-DRG as a principal diagnosis.
About the condition
Plain-language background from MedlinePlus (National Library of Medicine), not coding guidance.
Kidney Diseases
You have two kidneys, each about the size of your fist. They are near the middle of your back, just below the rib cage. Inside each kidney there are about a million tiny structures called nephrons. They filter your blood. They remove wastes and extra water, which become urine. The urine flows through tubes called ureters. It goes to your bladder, which stores the urine until you go to the bathroom.
Read more about kidney diseases on MedlinePlus