Other congenital malformations of the digestive system (Q38-Q45)
chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities
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Official coding guidelines
From the ICD-10-CM Official Guidelines for Coding and Reporting, FY 2027 (CMS and NCHS). Links open the PDF at the right page.
Assign Q00-QA1 codes for documented congenital anomalies or genetic disorders at any age, coding non-inherent manifestations separately and sequencing Z38 first on the birth admission.
All codes under Q38-Q45
Q38-Q45 can't be used on a claim. Pick a billable code below; grey headings group them.
- Q38Other congenital malformations of tongue, mouth and pharynx
- Q38.0Congenital malformations of lips, not elsewhere classified
- Q38.1Ankyloglossia
- Q38.2Macroglossia
- Q38.3Other congenital malformations of tongue
- Q38.4Congenital malformations of salivary glands and ducts
- Q38.5Congenital malformations of palate, not elsewhere classified
- Q38.6Other congenital malformations of mouth
- Q38.7Congenital pharyngeal pouch
- Q38.8Other congenital malformations of pharynx
- Q39Congenital malformations of esophagus
- Q39.0Atresia of esophagus without fistula
- Q39.1Atresia of esophagus with tracheo-esophageal fistula
- Q39.2Congenital tracheo-esophageal fistula without atresia
- Q39.3Congenital stenosis and stricture of esophagus
- Q39.4Esophageal web
- Q39.5Congenital dilatation of esophagus
- Q39.6Congenital diverticulum of esophagus
- Q39.8Other congenital malformations of esophagus
- Q39.9Congenital malformation of esophagus, unspecified
- Q40Other congenital malformations of upper alimentary tract
- Q40.0Congenital hypertrophic pyloric stenosis
- Q40.1Congenital hiatus hernia
- Q40.2Other specified congenital malformations of stomach
- Q40.3Congenital malformation of stomach, unspecified
- Q40.8Other specified congenital malformations of upper alimentary tract
- Q40.9Congenital malformation of upper alimentary tract, unspecified
- Q41Congenital absence, atresia and stenosis of small intestine
- Q41.0Congenital absence, atresia and stenosis of duodenum
- Q41.1Congenital absence, atresia and stenosis of jejunum
- Q41.2Congenital absence, atresia and stenosis of ileum
- Q41.8Congenital absence, atresia and stenosis of other specified parts of small intestine
- Q41.9Congenital absence, atresia and stenosis of small intestine, part unspecified
- Q42Congenital absence, atresia and stenosis of large intestine
- Q42.0Congenital absence, atresia and stenosis of rectum with fistula
- Q42.1Congenital absence, atresia and stenosis of rectum without fistula
- Q42.2Congenital absence, atresia and stenosis of anus with fistula
- Q42.3Congenital absence, atresia and stenosis of anus without fistula
- Q42.8Congenital absence, atresia and stenosis of other parts of large intestine
- Q42.9Congenital absence, atresia and stenosis of large intestine, part unspecified
- Q43Other congenital malformations of intestine
- Q43.0Meckel's diverticulum (displaced) (hypertrophic)
- Q43.1Hirschsprung's disease
- Q43.2Other congenital functional disorders of colon
- Q43.3Congenital malformations of intestinal fixation
- Q43.4Duplication of intestine
- Q43.5Ectopic anus
- Q43.6Congenital fistula of rectum and anus
- Q43.7Persistent cloaca
- Q43.8Other specified congenital malformations of intestine
- Q43.9Congenital malformation of intestine, unspecified
- Q44Congenital malformations of gallbladder, bile ducts and liver
- Q44.0Agenesis, aplasia and hypoplasia of gallbladder
- Q44.1Other congenital malformations of gallbladder
- Q44.2Atresia of bile ducts
- Q44.3Congenital stenosis and stricture of bile ducts
- Q44.4Choledochal cyst
- Q44.5Other congenital malformations of bile ducts
- Q44.6Cystic disease of liver
- Q44.7Other congenital malformations of liver
- Q44.70Other congenital malformation of liver, unspecified
- Q44.71Alagille syndrome
- Q44.79Other congenital malformations of liver
- Q45Other congenital malformations of digestive system
- Q45.0Agenesis, aplasia and hypoplasia of pancreas
- Q45.1Annular pancreas
- Q45.2Congenital pancreatic cyst
- Q45.3Other congenital malformations of pancreas and pancreatic duct
- Q45.8Other specified congenital malformations of digestive system
- Q45.9Congenital malformation of digestive system, unspecified
Q38-Q45 MS-DRGs
This code does not group to an MS-DRG as a principal diagnosis.
About the condition
Plain-language background from MedlinePlus (National Library of Medicine), not coding guidance.
Birth Defects
A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.
Read more about birth defects on MedlinePlusMouth Disorders
Your mouth is one of the most important parts of your body. It has many different functions. It allows you to: Any problem that affects your mouth can make it hard to eat, drink, or even smile. Some common mouth problems include:
Read more about mouth disorders on MedlinePlus